Literature DB >> 23522894

Clinical characteristics and management of iron overload in 631 patients with chronic transfusion dependency: results from a multicentre, observational study.

Joan Cid1, Luis Palomera2, Matías Díaz3, Concha Zamora4, Fernando Solano5.   

Abstract

BACKGROUND: Long-term red blood cell transfusion therapy results in iron overload. Consensus documents have been developed for several transfusion-dependent groups of patients to provide clinicians with guidance on the monitoring and treatment of this transfusion complication. The objective of this study was to describe the clinical characteristics and current standard of care for patients with transfusion dependency in Spain.
MATERIAL AND METHODS: This observational, multicentre study was conducted from November 2008 to December 2009 in 41 Spanish hospitals and day-care centres. Patients who received their first transfusion after January 2007, and who had received at least 10 units of packed red blood cells at the time of inclusion were eligible for the study.
RESULTS: We collected data from 631 patients with a mean age of 65±17 years. Haematological disease (84% of patients) was the most frequent underlying disorder. Patients had received a mean of 30±26 red blood cell units from diagnosis until inclusion in the study, and a mean of 18±18 red blood cell units in the previous year. Ferritin levels were available before and after starting the study for 116 (18%) and 412 (65%) patients, respectively. Mean ferritin level at study inclusion was 1,570 ng/mL, and 58% of patients had a ferritin level of at least 1,000 ng/mL. In spite of this, only 89 (14%) patients were receiving chelation therapy. DISCUSSION: The management of patients with transfusion dependency could be improved by using ferritin levels to diagnose iron overload and guide the timely start of chelation therapy.

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Year:  2013        PMID: 23522894      PMCID: PMC3934237          DOI: 10.2450/2013.0173-12

Source DB:  PubMed          Journal:  Blood Transfus        ISSN: 1723-2007            Impact factor:   3.443


  25 in total

Review 1.  Management of transfusional iron overload in Latin America: current outlook and expert panel recommendations.

Authors:  Aderson Araújo; Guillermo Drelichman; Rodolfo D Cançado; Nora Watman; Silvia M M Magalhães; Mauricio Duhalde; Javier Marfil; Aurora Feliú; Landolfi Clementina; Adriana Linares Ballesteros; Marco Di Stefano
Journal:  Hematology       Date:  2009-02       Impact factor: 2.269

2.  Italian Society of Hematology practice guidelines for the management of iron overload in thalassemia major and related disorders.

Authors:  Emanuele Angelucci; Giovanni Barosi; Clara Camaschella; Maria Domenica Cappellini; Mario Cazzola; Renzo Galanello; Monia Marchetti; Antonio Piga; Sante Tura
Journal:  Haematologica       Date:  2008-04-15       Impact factor: 9.941

3.  Transfusion-dependency at presentation and its acquisition in the first year of diagnosis are both equally detrimental for survival in primary myelofibrosis--prognostic relevance is independent of IPSS or karyotype.

Authors:  Ayalew Tefferi; Sergio Siragusa; Kebede Hussein; Susan M Schwager; Curtis A Hanson; Animesh Pardanani; Francisco Cervantes; Francesco Passamonti
Journal:  Am J Hematol       Date:  2010-01       Impact factor: 10.047

4.  Clinical management of myelodysplastic syndromes: update of SIE, SIES, GITMO practice guidelines.

Authors:  V Santini; P E Alessandrino; E Angelucci; G Barosi; A Billio; M Di Maio; C Finelli; F Locatelli; M Marchetti; E Morra; P Musto; G Visani; S Tura
Journal:  Leuk Res       Date:  2010-02-11       Impact factor: 3.156

5.  Impact of the degree of anemia on the outcome of patients with myelodysplastic syndrome and its integration into the WHO classification-based Prognostic Scoring System (WPSS).

Authors:  Luca Malcovati; Matteo G Della Porta; Corinna Strupp; Ilaria Ambaglio; Andrea Kuendgen; Kathrin Nachtkamp; Erica Travaglino; Rosangela Invernizzi; Cristiana Pascutto; Mario Lazzarino; Ulrich Germing; Mario Cazzola
Journal:  Haematologica       Date:  2011-06-09       Impact factor: 9.941

6.  What are RBC-transfusion-dependence and -independence?

Authors:  R P Gale; G Barosi; T Barbui; F Cervantes; K Dohner; B Dupriez; V Gupta; C Harrison; R Hoffman; J-J Kiladjian; R Mesa; M F Mc Mullin; F Passamonti; V Ribrag; G Roboz; G Saglio; A Vannucchi; S Verstovsek
Journal:  Leuk Res       Date:  2010-08-07       Impact factor: 3.156

Review 7.  Guidelines on iron chelation therapy in patients with myelodysplastic syndromes and transfusional iron overload.

Authors:  Norbert Gattermann
Journal:  Leuk Res       Date:  2007-12       Impact factor: 3.156

8.  Impact of transfusion dependency on survival in patients with early myelodysplastic syndrome without excess of blasts.

Authors:  Jaroslav Cermak; Petra Kacirkova; Dana Mikulenkova; Kyra Michalova
Journal:  Leuk Res       Date:  2009-07-30       Impact factor: 3.156

9.  Two regression models and a scoring system for predicting survival and planning treatment in myelodysplastic syndromes: a multivariate analysis of prognostic factors in 370 patients.

Authors:  G F Sanz; M A Sanz; T Vallespí; M C Cañizo; M Torrabadella; S García; D Irriguible; J F San Miguel
Journal:  Blood       Date:  1989-07       Impact factor: 22.113

10.  Diagnosing and treating Diamond Blackfan anaemia: results of an international clinical consensus conference.

Authors:  Adrianna Vlachos; Sarah Ball; Niklas Dahl; Blanche P Alter; Sujit Sheth; Ugo Ramenghi; Joerg Meerpohl; Stefan Karlsson; Johnson M Liu; Thierry Leblanc; Carole Paley; Elizabeth M Kang; Eva Judmann Leder; Eva Atsidaftos; Akiko Shimamura; Monica Bessler; Bertil Glader; Jeffrey M Lipton
Journal:  Br J Haematol       Date:  2008-07-30       Impact factor: 6.998

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