OBJECTIVE: To report the clinical, neuropsychological, linguistic, imaging, and neuropathological features of a unique case of sporadic Jakob-Creutzfeldt disease in which the patient presented with a logopenic variant of primary progressive aphasia. DESIGN: Case report. SETTING: Large referral center for atypical memory and aging disorders, particularly Jakob-Creutzfeldt disease. PATIENT: Patient presenting with logopenic variant primary progressive aphasia initially thought to be due to Alzheimer disease. RESULTS: Despite the long, slow 3.5-year course, the patient was shown to have pathology-proven sporadic Jakob-Creutzfeldt disease. CONCLUSIONS: These findings expand the differential of primary progressive aphasia to include prion disease.
OBJECTIVE: To report the clinical, neuropsychological, linguistic, imaging, and neuropathological features of a unique case of sporadic Jakob-Creutzfeldt disease in which the patient presented with a logopenic variant of primary progressive aphasia. DESIGN: Case report. SETTING: Large referral center for atypical memory and aging disorders, particularly Jakob-Creutzfeldt disease. PATIENT: Patient presenting with logopenic variant primary progressive aphasia initially thought to be due to Alzheimer disease. RESULTS: Despite the long, slow 3.5-year course, the patient was shown to have pathology-proven sporadic Jakob-Creutzfeldt disease. CONCLUSIONS: These findings expand the differential of primary progressive aphasia to include prion disease.
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