| Literature DB >> 23187718 |
Melissa A Klausmeyer1, Myles J Cohen, David A Kulber.
Abstract
Ollier disease is a nonhereditary disorder characterized by multiple enchondromata, with a random asymmetrical distribution. We report an unusual case of massive ulcerating multiple enchondromata of the left hand of an 11-year-old male patient. A methodical approach to treating such a massive tumor burden and steps in reconstructing the hand are described. This case report demonstrates a radical expression of this disease; however, no malignancy was identified despite the aggressive and chronic nature of the disease. Unlike previously reported cases with less severe involvement, this patient did not undergo amputation, and this approach demonstrates a strategy for limb salvage not previously described. In particular, despite bony defects of 6 cm, no autograph was necessary for the reconstruction of the hand.Entities:
Mesh:
Year: 2013 PMID: 23187718 DOI: 10.1097/SAP.0b013e318255a3ce
Source DB: PubMed Journal: Ann Plast Surg ISSN: 0148-7043 Impact factor: 1.539