Literature DB >> 23036572

Laser clearance of drusen deposit in patients with autosomal dominant drusen (p.Arg345Trp in EFEMP1).

Eva Lenassi1, Eric Troeger, Robert Wilke, Adnan Tufail, Marko Hawlina, Glen Jeffery, Andrew R Webster.   

Abstract

PURPOSE: To assess whether laser treatment to the retinal pigment epithelium anterior to drusen in eyes of patients with EFEMP1-related maculopathy affects visual acuity, deposit volume, and retinal sensitivity.
DESIGN: Prospective, interventional case series.
METHODS: In 11 patients with autosomal dominant drusen and confirmed disease-causing EFEMP1 mutation, the worse-seeing eye was treated with Argon green laser (10 to 15 laser spots; 200-μm spot size, 0.1-second duration, 80 to 120 mW). Patients were examined before treatment as well as 1, 3, 6, and 12 months after the procedure. Clinical assessment included visual acuity, fundus-controlled perimetry, spectral-domain optical coherence tomography, and autofluorescence imaging. Custom-made software allowed for coregistration of fundus-controlled perimetry and spectral-domain optical coherence tomography data sets. The main outcome measures were change in visual acuity, retinal sensitivity, and drusen volume.
RESULTS: The untreated eyes lost an average of 0.8 letters, whereas the treated eyes gained an average of 4.9 letters. For fundus-controlled perimetry, locus-by-locus differences in sensitivity were calculated between pretreatment and posttreatment assessments; subsequently, the overall difference in the treated and untreated eye was compared. Five patients showed significant improvement in retinal sensitivity, 5 patients showed no change, and 1 patient showed significant deterioration. An increase in mean drusen thickness was observed in the untreated eyes, but not in the treated eyes (P = .0322). The thickness of the drusen correlated with retinal sensitivity (ρ = -0.49; P < .0001). Safety was demonstrated and no adverse events were observed.
CONCLUSIONS: Low-energy laser treatment is safe and may be effective in the treatment of autosomal dominant drusen. Further evaluation with long-term assessment is required to confirm the benefits.
Copyright © 2013 Elsevier Inc. All rights reserved.

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Year:  2012        PMID: 23036572     DOI: 10.1016/j.ajo.2012.07.003

Source DB:  PubMed          Journal:  Am J Ophthalmol        ISSN: 0002-9394            Impact factor:   5.258


  4 in total

1.  The second Japanese family with Malattia Leventinese/Doyne honeycomb retinal dystrophy.

Authors:  Nobuko Enomoto; Takaaki Hayashi; Tomokazu Matsuura; Koji Tanaka; Remi Takeuchi; Goji Tomita; Ryusaburo Mori
Journal:  Doc Ophthalmol       Date:  2021-11-25       Impact factor: 2.379

2.  Comparison of drusen and modifying genes in autosomal dominant radial drusen and age-related macular degeneration.

Authors:  Elliott H Sohn; Kai Wang; Stewart Thompson; Megan J Riker; Jeremy M Hoffmann; Edwin M Stone; Robert F Mullins
Journal:  Retina       Date:  2015-01       Impact factor: 4.256

Review 3.  Clinical Perspectives and Trends: Microperimetry as a Trial Endpoint in Retinal Disease.

Authors:  Yesa Yang; Hannah Dunbar
Journal:  Ophthalmologica       Date:  2021-02-10       Impact factor: 3.250

4.  First reported case of Doyne honeycomb retinal dystrophy (Malattia Leventinese/autosomal dominant drusen) in Scandinavia.

Authors:  Inger Norlyk Sheyanth; Ihab Bishara Lolas; Henrik Okkels; Ligor Pradeep Kiruparajan; Søren Kromann Abildgaard; Michael Bjørn Petersen
Journal:  Mol Genet Genomic Med       Date:  2021-03-10       Impact factor: 2.183

  4 in total

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