Literature DB >> 22863689

Vitamin D in children with cystic fibrosis.

Malcolm Brodlie1, William A Orchard, Gordon A Reeks, Stewart Pattman, Helen McCabe, Christopher J O'Brien, Matthew F Thomas, David Anthony Spencer.   

Abstract

PURPOSE: The Cystic Fibrosis Trust in 2007 published a recommended target of 75-150 nmol/L for 25-hydroxyvitamin D (25-OHD). In 2008 we found that only 10% of pancreatic insufficient (PI) children met this target. An increase in supplementation was implemented and a repeat audit performed in 2010.
METHODS: PI children ≥1 year under sole-care in our regional centre were included. Vitamin D3 supplementation increased by >450% to either 3800 IU/day liquid or 800 IU daily plus 20,000 IU weekly tablets. In 2010 pancreatic sufficient (PS) children were also audited separately.
RESULTS: The median 25-OHD level increased from 51.5 nmol/L in 2008 (n=78, 10% >75 nmol/L) to 72 nmol/L in 2010 (n=72, 51% >75 nmol/L), p<0.0001. In PS children (n=15 in 2010) 87% had 25-OHD levels <75 nmol/L.
CONCLUSIONS: A substantial increase in supplementation led to a significant increase in 25-OHD levels but around half still failed to reach the recommended target.

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Year:  2012        PMID: 22863689     DOI: 10.1136/archdischild-2011-301398

Source DB:  PubMed          Journal:  Arch Dis Child        ISSN: 0003-9888            Impact factor:   3.791


  7 in total

1.  Relationship Between Fat-Soluble Vitamin Supplementation and Blood Concentrations in Adolescent and Adult Patients With Cystic Fibrosis.

Authors:  Oranan Siwamogsatham; Wei Dong; Jose N Binongo; Ritam Chowdhury; Jessica A Alvarez; Shawna J Feinman; Jessica Enders; Vin Tangpricha
Journal:  Nutr Clin Pract       Date:  2014-04-17       Impact factor: 3.080

Review 2.  Diagnosis and treatment of endocrine comorbidities in patients with cystic fibrosis.

Authors:  Oranan Siwamogsatham; Jessica A Alvarez; Vin Tangpricha
Journal:  Curr Opin Endocrinol Diabetes Obes       Date:  2014-10       Impact factor: 3.243

3.  Fat-soluble vitamins in cystic fibrosis and pancreatic insufficiency: efficacy of a nutrition intervention.

Authors:  Chiara Bertolaso; Veronique Groleau; Joan I Schall; Asim Maqbool; Maria Mascarenhas; Norma E Latham; Kelly A Dougherty; Virginia A Stallings
Journal:  J Pediatr Gastroenterol Nutr       Date:  2014-04       Impact factor: 2.839

4.  Are Vitamin D3 Tablets and Oil Drops Equally Effective in Raising S-25-Hydroxyvitamin D Concentrations? A Post-Hoc Analysis of an Observational Study on Immunodeficient Patients.

Authors:  Maria Helde Frankling; Anna-Carin Norlin; Susanne Hansen; Emilie Wahren Borgström; Peter Bergman; Linda Björkhem-Bergman
Journal:  Nutrients       Date:  2020-04-26       Impact factor: 5.717

Review 5.  Update on the management of vitamins and minerals in cystic fibrosis.

Authors:  Senthilkumar Sankararaman; Sara J Hendrix; Terri Schindler
Journal:  Nutr Clin Pract       Date:  2022-08-23       Impact factor: 3.204

6.  Treatment of cystic fibrosis related bone disease.

Authors:  Jagdeesh Ullal; Katherine Kutney; Kristen M Williams; David R Weber
Journal:  J Clin Transl Endocrinol       Date:  2021-12-21

7.  Vitamin D Status in Pediatric and Young Adult Cystic Fibrosis Patients. Are the New Recommendations Effective?

Authors:  Carmen Mangas-Sánchez; María Garriga-García; María Juliana Serrano-Nieto; Ruth García-Romero; Marina Álvarez-Beltrán; Elena Crehuá-Gaudiza; Rosana Muñoz-Codoceo; Lucrecia Suárez-Cortina; Saioa Vicente-Santamaría; Cecilia Martínez-Costa; Juan José Díaz-Martin; Carlos Bousoño-García; David González-Jiménez
Journal:  Nutrients       Date:  2021-12-09       Impact factor: 5.717

  7 in total

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