Literature DB >> 22803838

RET/PTC rearrangement is prevalent in follicular Hürthle cell carcinomas.

Margriet M de Vries1, Ricardo Celestino, Patricia Castro, Catarina Eloy, Valdemar Máximo, Jacqueline E van der Wal, John T M Plukker, Thera P Links, Robert M W Hofstra, Manuel Sobrinho-Simões, Paula Soares.   

Abstract

AIMS: The molecular alterations underlying follicular Hürthle cell carcinomas (FHCCs) are largely unknown. In an attempt to clarify this issue, we analysed a series of Hürthle cell tumours for the presence of RET/PTC and PAX8/PPARG rearrangements and BRAF, HRAS and NRAS mutations. METHODS AND
RESULTS: We investigated a series of 20 follicular Hürthle cell tumours [17 FHCCs and three follicular Hürthle cell adenomas (FHCAs)]. RET/PTC rearrangements were found in 33% of FHCAs and in 38% of FHCCs. All RET/PTC-positive FHCCs had a solid pattern of growth. PAX8/PPARG rearrangement was present in 27% of the FHCCs which displayed, in most cases, a follicular architecture. NRAS mutation was detected in one FHCC. An FHCC with a solid/microfollicular growth pattern scored positive for both RET/PTC and PAX8/PPARG rearrangement.
CONCLUSIONS: Our study has shown a significant association between RET/PTC rearrangements and FHCCs with a solid growth pattern, thus raising the possibility of using tyrosine kinase inhibitors for the treatment of patients with FHCCs, which are often refractory to radioiodine treatment.
© 2012 Blackwell Publishing Limited.

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Year:  2012        PMID: 22803838     DOI: 10.1111/j.1365-2559.2012.04276.x

Source DB:  PubMed          Journal:  Histopathology        ISSN: 0309-0167            Impact factor:   5.087


  11 in total

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9.  mTOR Pathway in Papillary Thyroid Carcinoma: Different Contributions of mTORC1 and mTORC2 Complexes for Tumor Behavior and SLC5A5 mRNA Expression.

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Authors:  David G McFadden; Peter M Sadow
Journal:  Front Endocrinol (Lausanne)       Date:  2021-06-10       Impact factor: 6.055

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