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35 in total

1. Ion channel formation by duramycin.

Authors: T R Sheth; R M Henderson; S B Hladky; A W Cuthbert
Journal: Biochim Biophys Acta Date: 1992-06-11

Review 2. Molecular mechanisms of CFTR chloride channel dysfunction in cystic fibrosis.

Authors: M J Welsh; A E Smith
Journal: Cell Date: 1993-07-02 Impact factor: 41.582

3. Inhalation of amiloride improves the mucociliary and the cough clearance in patients with cystic fibroses.

Authors: D Köhler; E App; M Schmitz-Schumann; G Würtemberger; H Matthys
Journal: Eur J Respir Dis Suppl Date: 1986

4. Duramycin enhances chloride secretion in airway epithelium.

Authors: M M Cloutier; L Guernsey; P Mattes; B Koeppen
Journal: Am J Physiol Date: 1990-09

5. French multicenter randomized double-blind placebo-controlled trial on nebulized amiloride in cystic fibrosis patients. The Amiloride-AFLM Collaborative Study Group.

Authors: G Pons; M C Marchand; P d'Athis; E Sauvage; C Foucard; P Chaumet-Riffaud; A Sautegeau; J Navarro; G Lenoir
Journal: Pediatr Pulmonol Date: 2000-07

6. Structure of nucleotide-binding domain 1 of the cystic fibrosis transmembrane conductance regulator.

Authors: Hal A Lewis; Sean G Buchanan; Stephen K Burley; Kris Conners; Mark Dickey; Michael Dorwart; Richard Fowler; Xia Gao; William B Guggino; Wayne A Hendrickson; John F Hunt; Margaret C Kearins; Don Lorimer; Peter C Maloney; Kai W Post; Kanagalaghatta R Rajashankar; Marc E Rutter; J Michael Sauder; Stephanie Shriver; Patrick H Thibodeau; Philip J Thomas; Marie Zhang; Xun Zhao; Spencer Emtage
Journal: EMBO J Date: 2003-12-18 Impact factor: 11.598

7. Relative ion permeability of normal and cystic fibrosis nasal epithelium.

Authors: M Knowles; J Gatzy; R Boucher
Journal: J Clin Invest Date: 1983-05 Impact factor: 14.808

8. Stimulation of sodium transport by duramycin in cultured human colonic epithelia.

Authors: M Roberts; S B Hladky; R J Pickles; A W Cuthbert
Journal: J Pharmacol Exp Ther Date: 1991-12 Impact factor: 4.030

9. Pharmacological properties of N-(3,5-diamino-6-chloropyrazine-2-carbonyl)-N'-4-[4-(2,3-dihydroxypropoxy)phenyl]butyl-guanidine methanesulfonate (552-02), a novel epithelial sodium channel blocker with potential clinical efficacy for cystic fibrosis lung disease.

Authors: Andrew J Hirsh; Jim Zhang; Andra Zamurs; Jacquelyn Fleegle; William R Thelin; Ray A Caldwell; Juan R Sabater; William M Abraham; Mark Donowitz; Boyoung Cha; Kevin B Johnson; Judith A St George; M Ross Johnson; Richard C Boucher
Journal: J Pharmacol Exp Ther Date: 2008-01-24 Impact factor: 4.030

Cystic fibrosis transmembrane conductance regulator dysfunction and its treatment.

1. Ion channel formation by duramycin.

Review 2. Molecular mechanisms of CFTR chloride channel dysfunction in cystic fibrosis.

3. Inhalation of amiloride improves the mucociliary and the cough clearance in patients with cystic fibroses.

4. Duramycin enhances chloride secretion in airway epithelium.

5. French multicenter randomized double-blind placebo-controlled trial on nebulized amiloride in cystic fibrosis patients. The Amiloride-AFLM Collaborative Study Group.

6. Structure of nucleotide-binding domain 1 of the cystic fibrosis transmembrane conductance regulator.

7. Relative ion permeability of normal and cystic fibrosis nasal epithelium.

8. Stimulation of sodium transport by duramycin in cultured human colonic epithelia.

9. Pharmacological properties of N-(3,5-diamino-6-chloropyrazine-2-carbonyl)-N'-4-[4-(2,3-dihydroxypropoxy)phenyl]butyl-guanidine methanesulfonate (552-02), a novel epithelial sodium channel blocker with potential clinical efficacy for cystic fibrosis lung disease.

10. No added benefit from nebulized amiloride in patients with cystic fibrosis.

Review 1. An Intriguing Involvement of Mitochondria in Cystic Fibrosis.

2. Reduced Expression of TMEM16A Impairs Nitric Oxide-Dependent Cl^- Transport in Retinal Amacrine Cells.

3. Association between clinical antibiotic resistance and susceptibility of Pseudomonas in the cystic fibrosis lung.