Literature DB >> 22514587

Adams-Oliver Syndrome. A case with isolated aplasia cutis congenita and skeletal defects.

Ola Bakry1, Abdalla Attia, Eman Nabil El Shafey.   

Abstract

BACKGROUND: Adams-Oliver Syndrome is characterized by the combination of aplasia cutis congenita and limb anomalies. It was initially described in 1945 by Adams and Oliver. MAIN OBSERVATIONS: We report a case of a 10-year-old girl with Adams-Oliver Syndrome with aplasia cutis congenita and limb defects only with no internal organ anomalies.
CONCLUSIONS: Adams-Oliver Syndrome is a rare multisystem disorder of unknown etiology. It may be presented by isolated aplasia cutis congenita and limb anomalies.

Entities:  

Keywords:  Adams-Oliver syndrome; aplasia cutis; cicatricial alopecia; limb defects; scarring alopecia

Year:  2012        PMID: 22514587      PMCID: PMC3322107          DOI: 10.3315/jdcr.2012.1092

Source DB:  PubMed          Journal:  J Dermatol Case Rep        ISSN: 1898-7249


  21 in total

1.  Clinical evidence of vascular abnormalities at birth in Adams-Oliver syndrome: report of two further cases.

Authors:  L Pereira-Da-Silva; F Leal; G C Santos; J M Videira Amaral; M J Feijóo
Journal:  Am J Med Genet       Date:  2000-09-04

Review 2.  Adams-Oliver syndrome: genetics and associated anomalies of cutis aplasia.

Authors:  T J Pousti; R A Bartlett
Journal:  Plast Reconstr Surg       Date:  1997-11       Impact factor: 4.730

Review 3.  Congenital scalp defects with distal limb anomalies (Adams-Oliver syndrome): report of ten cases and review of the literature.

Authors:  W Küster; W Lenz; H Kääriäinen; F Majewski
Journal:  Am J Med Genet       Date:  1988-09

Review 4.  The wide spectrum of clinical expression in Adams-Oliver syndrome: a report of two cases.

Authors:  M Mempel; D Abeck; I Lange; K Strom; A Caliebe; A Beham; M Kautza; W I Worret; B A Neubauer; J Ring; H Schröder; R Fölster-Holst
Journal:  Br J Dermatol       Date:  1999-06       Impact factor: 9.302

5.  A case of adams-oliver syndrome.

Authors:  Jong-Keun Seo; Ju-Hyun Kang; Hyun-Jae Lee; Deborah Lee; Ho-Suk Sung; Seon-Wook Hwang
Journal:  Ann Dermatol       Date:  2010-02-28       Impact factor: 1.444

6.  Congenital scalp skull defects with distal limb anomalies (Adams-Oliver syndrome--McKusick 10030): further suggestion of autosomal recessive inheritance.

Authors:  C P Koiffmann; A Wajntal; B J Huyke; R M Castro
Journal:  Am J Med Genet       Date:  1988-02

7.  Aplasia cutis congenita, terminal limb defects and falciform retinal folds: confirmation of a distinct syndrome of vascular disruption.

Authors:  Joanna Prothero; Richard Nicholl; Judith Wilson; Emma L Wakeling
Journal:  Clin Dysmorphol       Date:  2007-01       Impact factor: 0.816

8.  Adams-Oliver syndrome: a case with juvenile chronic myelogenous leukemia and chylothorax.

Authors:  S A Farrell; L J Warda; P LaFlair; W Szymonowicz
Journal:  Am J Med Genet       Date:  1993-12-01

9.  Vascular pathogenesis of transverse limb reduction defects.

Authors:  H E Hoyme; K L Jones; M I Van Allen; B S Saunders; K Benirschke
Journal:  J Pediatr       Date:  1982-11       Impact factor: 4.406

10.  Vascular abnormalities in Adams-Oliver syndrome: cause or effect?

Authors:  E N Swartz; S Sanatani; G G Sandor; R A Schreiber
Journal:  Am J Med Genet       Date:  1999-01-01
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  5 in total

1.  [Circumscribed aplasia cutis congenita of the scalp in a Rwandan child: about an observation].

Authors:  Olga Ntumba-Tshitenge; Célestin Kaputu-Kalala-Malu; Caritas Mukampunga; Kavulu Mayamba Mukendi
Journal:  Pan Afr Med J       Date:  2014-10-29

2.  Adams-Oliver Syndrome: A Case with Full Expression.

Authors:  Amir Dehdashtian; Masoud Dehdashtian
Journal:  Pediatr Rep       Date:  2016-06-27

Review 3.  Case report and review of literature of a rare congenital disorder: Adams-Oliver syndrome.

Authors:  Edwin Suarez; Mia J Bertoli; Jean Daniel Eloy; Shridevi Pandya Shah
Journal:  BMC Anesthesiol       Date:  2021-04-15       Impact factor: 2.217

4.  Adams-Oliver syndrome, intestinal obstruction and heart defects: a case series of aplasia cutis congenita.

Authors:  Ihsan Baroudi; Ola Alakhras; Thaer Douri; Nedal Alkhani
Journal:  Oxf Med Case Reports       Date:  2022-01-24

5.  Adams-Oliver Syndrome: A Rare Congenital Disorder.

Authors:  Sumara Rashid; Saleha Azeem; Samiha Riaz
Journal:  Cureus       Date:  2022-03-18
  5 in total

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