Literature DB >> 22419577

Hematologic responses to deferasirox therapy in transfusion-dependent patients with myelodysplastic syndromes.

Norbert Gattermann1, Carlo Finelli, Matteo Della Porta, Pierre Fenaux, Michael Stadler, Agnes Guerci-Bresler, Mathias Schmid, Kerry Taylor, Dominique Vassilieff, Dany Habr, Andrea Marcellari, Bernard Roubert, Christian Rose.   

Abstract

BACKGROUND: Reductions in transfusion requirements/improvements in hematologic parameters have been associated with iron chelation therapy in transfusion-dependent patients, including those with myelodysplastic syndromes; data on there reductions/improvements have been limited to case reports and small studies. DESIGN AND METHODS: To explore this observation in a large population of patients, we report a post-hoc analysis evaluating hematologic response to deferasirox in a cohort of iron-overloaded patients with myelodysplastic syndromes enrolled in the Evaluation of Patients' Iron Chelation with Exjade(®) (EPIC) study using International Working Group 2006 criteria.
RESULTS: Two-hundred and forty-seven, 100 and 50 patients without concomitant medication for myelodysplastic syndromes were eligible for analysis of erythroid, platelet and neutrophil responses, respectively. Erythroid, platelet and neutrophil responses were observed in 21.5% (53/247), 13.0% (13/100) and 22.0% (11/50) of the patients after a median of 109, 169 and 226 days, respectively. Median serum ferritin reductions were greater in hematologic responders compared with non-responders at end of study, although these differences were not statistically significant. A reduction in labile plasma iron to less than 0.4 μmol/L was observed from week 12 onwards; this change did not differ between hematologic responders and non-responders.
CONCLUSIONS: This analysis suggests that deferasirox treatment for up to 1 year could lead to improvement in hematologic parameters in some patients with myelodysplastic syndromes.

Entities:  

Mesh:

Substances:

Year:  2012        PMID: 22419577      PMCID: PMC3436237          DOI: 10.3324/haematol.2011.048546

Source DB:  PubMed          Journal:  Haematologica        ISSN: 0390-6078            Impact factor:   9.941


  39 in total

1.  Deferasirox in iron-overloaded patients with transfusion-dependent myelodysplastic syndromes: Results from the large 1-year EPIC study.

Authors:  Norbert Gattermann; Carlo Finelli; Matteo Della Porta; Pierre Fenaux; Arnold Ganser; Agnes Guerci-Bresler; Mathias Schmid; Kerry Taylor; Dominique Vassilieff; Dany Habr; Gabor Domokos; Bernard Roubert; Christian Rose
Journal:  Leuk Res       Date:  2010-05-06       Impact factor: 3.156

2.  Desferrioxamine treatment reduces blood transfusion requirements in patients with myelodysplastic syndrome.

Authors:  P D Jensen; I M Jensen; J Ellegaard
Journal:  Br J Haematol       Date:  1992-01       Impact factor: 6.998

3.  Changes in parameters of oxidative stress and free iron biomarkers during treatment with deferasirox in iron-overloaded patients with myelodysplastic syndromes.

Authors:  Hussam Ghoti; Eitan Fibach; Drorit Merkel; Galit Perez-Avraham; Sigal Grisariu; Eliezer A Rachmilewitz
Journal:  Haematologica       Date:  2010-04-26       Impact factor: 9.941

4.  Iron chelation therapy in patients with myelodysplastic syndromes: consensus conference guidelines.

Authors:  Moshe Mittelman; Gilles Lugassy; Drorit Merkel; Hannah Tamary; Nadav Sarid; Eliezer Rachmilewitz; Chaim Hershko
Journal:  Isr Med Assoc J       Date:  2008-05       Impact factor: 0.892

5.  Clinical application and proposal for modification of the International Working Group (IWG) response criteria in myelodysplasia.

Authors:  Bruce D Cheson; Peter L Greenberg; John M Bennett; Bob Lowenberg; Pierre W Wijermans; Stephen D Nimer; Antonio Pinto; Miloslav Beran; Theo M de Witte; Richard M Stone; Moshe Mittelman; Guillermo F Sanz; Steven D Gore; Charles A Schiffer; Hagop Kantarjian
Journal:  Blood       Date:  2006-04-11       Impact factor: 22.113

6.  Deferasirox reduces serum ferritin and labile plasma iron in RBC transfusion-dependent patients with myelodysplastic syndrome.

Authors:  Alan F List; Maria R Baer; David P Steensma; Azra Raza; Jason Esposito; Noelia Martinez-Lopez; Carole Paley; John Feigert; Emmanuel Besa
Journal:  J Clin Oncol       Date:  2012-04-30       Impact factor: 44.544

Review 7.  Oxidative stress in the regulation of normal and neoplastic hematopoiesis.

Authors:  Saghi Ghaffari
Journal:  Antioxid Redox Signal       Date:  2008-11       Impact factor: 8.401

8.  Hematologic response to three alternative dosing schedules of azacitidine in patients with myelodysplastic syndromes.

Authors:  Roger M Lyons; Thomas M Cosgriff; Sanjiv S Modi; Robert H Gersh; John D Hainsworth; Allen L Cohn; Heidi J McIntyre; Indra J Fernando; Jay T Backstrom; C L Beach
Journal:  J Clin Oncol       Date:  2009-03-02       Impact factor: 44.544

9.  Labile plasma iron in iron overload: redox activity and susceptibility to chelation.

Authors:  Breno P Esposito; William Breuer; Pornpan Sirankapracha; Pensri Pootrakul; Chaim Hershko; Z Ioav Cabantchik
Journal:  Blood       Date:  2003-06-12       Impact factor: 22.113

10.  Correction of anemia in a transfusion-dependent patient with primary myelofibrosis receiving iron chelation therapy with deferasirox (Exjade, ICL670).

Authors:  Anna Angela Di Tucci; Roberta Murru; Daniele Alberti; Bertrand Rabault; Simona Deplano; Emanuele Angelucci
Journal:  Eur J Haematol       Date:  2007-03-28       Impact factor: 2.997

View more
  48 in total

Review 1.  Iron chelation therapy in myelodysplastic syndromes: where do we stand?

Authors:  Mhairi Mitchell; Steven D Gore; Amer M Zeidan
Journal:  Expert Rev Hematol       Date:  2013-08       Impact factor: 2.929

2.  Deferasirox therapy is associated with reduced mortality risk in a medicare population with myelodysplastic syndromes.

Authors:  Amer M Zeidan; Franklin Hendrick; Erika Friedmann; Maria R Baer; Steven D Gore; Medha Sasane; Carole Paley; Amy J Davidoff
Journal:  J Comp Eff Res       Date:  2015-08       Impact factor: 1.744

3.  Haematological improvement as a beneficial effect during deferasirox treatment in transfusion-dependent patients with myelodysplastic syndrome.

Authors:  Matteo Molica; Adriano Salaroli; Giuliana Alimena; Massimo Breccia
Journal:  Blood Transfus       Date:  2013-04-15       Impact factor: 3.443

4.  A case of transfusion independence in a patient with myelodysplastic syndrome using deferasirox, sustained for two years after stopping therapy.

Authors:  D Sanford; C C Hsia
Journal:  Curr Oncol       Date:  2015-04       Impact factor: 3.677

5.  Long-term hematological response in a patient with 5q- syndrome after suspension of lenalidomide therapy and further improvement with deferasirox therapy.

Authors:  Pasquale Niscola; Andrea Tendas; Laura Scaramucci; Roberta Merola; Gianfranco Catalano; Paolo de Fabritiis
Journal:  Blood Res       Date:  2014-06-25

6.  Management of iron overload in myelodysplastic syndromes: combined deferasirox and deferoxamine in a patient with liver disease.

Authors:  Claudio Cerchione; Giuseppe Cerciello; Simona Avilia; Roberta Della Pepa; Novella Pugliese; Marco Picardi; Lucio Catalano; Fabrizio Pane
Journal:  Blood Transfus       Date:  2016-10-24       Impact factor: 3.443

7.  Differential effects of the type of iron chelator on the absolute number of hematopoietic peripheral progenitors in patients with β-thalassemia major.

Authors:  Gian Luca Forni; Marina Podestà; Marco Musso; Giovanna Piaggio; Khaled M Musallam; Manuela Balocco; Sarah Pozzi; Alessandra Rosa; Francesco Frassoni
Journal:  Haematologica       Date:  2012-12-14       Impact factor: 9.941

Review 8.  Iron overload in myelodysplastic syndromes (MDS).

Authors:  Norbert Gattermann
Journal:  Int J Hematol       Date:  2017-11-25       Impact factor: 2.490

9.  Hematologic responses in patients with aplastic anemia treated with deferasirox: a post hoc analysis from the EPIC study.

Authors:  Jong Wook Lee; Sung-Soo Yoon; Zhi Xiang Shen; Arnold Ganser; Hui-Chi Hsu; Ali El-Ali; Dany Habr; Nicolas Martin; John B Porter
Journal:  Haematologica       Date:  2013-04-12       Impact factor: 9.941

10.  Safety and efficacy of deferasirox in the management of transfusion-dependent patients with myelodysplastic syndrome and aplastic anaemia: a perspective review.

Authors:  Rebecca L C Adams; Robert J Bird
Journal:  Ther Adv Hematol       Date:  2013-04
View more

北京卡尤迪生物科技股份有限公司 © 2022-2023.