Harshad R Purandare1, Basant K Misra. 1. Department of Neurosurgery and Gamma Knife Radiosurgery, P D Hinduja National Hospital and Medical Research Centre, Mumbai, India.
Abstract
BACKGROUND: Hemangioblastomas are benign tumors that occur sporadically or as part of von Hippel-Lindau disease. Occasionally, they have an extramedullary location along the nerve roots and, rarely, are purely extradural. CASE DESCRIPTION: We report a rare case of a completely extradural large hemangioblastoma in a 32-year-old man presenting with radiculopathy and a posterior mediastinal mass. Screening revealed a similar tumor in the right cerebellar hemisphere. The patient underwent a right paramedian suboccipital craniotomy and total excision of the cerebellar tumor, followed by a left lateral thoracotomy and complete excision of the mediastinal lesion. The patient had an uneventful recovery. CONCLUSIONS: Hemangioblastomas should be considered in the diagnosis of posterior mediastinal tumors in the presence of typical imaging features or with associated intra-axial tumors, so as to plan preoperative angiography and embolization.
BACKGROUND:Hemangioblastomas are benign tumors that occur sporadically or as part of von Hippel-Lindau disease. Occasionally, they have an extramedullary location along the nerve roots and, rarely, are purely extradural. CASE DESCRIPTION: We report a rare case of a completely extradural large hemangioblastoma in a 32-year-old man presenting with radiculopathy and a posterior mediastinal mass. Screening revealed a similar tumor in the right cerebellar hemisphere. The patient underwent a right paramedian suboccipital craniotomy and total excision of the cerebellar tumor, followed by a left lateral thoracotomy and complete excision of the mediastinal lesion. The patient had an uneventful recovery. CONCLUSIONS:Hemangioblastomas should be considered in the diagnosis of posterior mediastinal tumors in the presence of typical imaging features or with associated intra-axial tumors, so as to plan preoperative angiography and embolization.