Literature DB >> 22379434

Hand and foot abnormalities associated with genetic diseases.

Henry J Mankin, Jesse Jupiter, Carol Ann Trahan.   

Abstract

INTRODUCTION: The small bones and soft tissues of the hands and feet can be affected by systemic disorders, and frequently, the findings are quite unique and virtually diagnostic for some genetic or metabolic disorders.
MATERIALS AND METHODS: Photographs and imaging studies for the hands and feet are available in a digitized system, which has been approved by our hospital institutional review board. Examination of these and their description can establish a relationship with some degree of certainty to a series of highly variable and uncommon clinical disorders.
RESULTS: Description of the clinical, physiologic and genetic characteristics, and illustrations of hand and foot abnormalities are provided for an array of diseases, including Ellis-van Creveld syndrome, fibrodysplasia ossificans progressiva, achondroplasia, Kniest dysplasia, pseudo- and pseudo-pseudohypoparathyroidism, acromegaly, nail-patella syndrome, Marfan's disease, cartilage-hair hypoplasia, and several forms of mucopolysaccharidosis.
CONCLUSIONS: The findings support the concept that many genetic disorders can often be diagnosed by clinical and imaging examination of the patient's hands and feet.

Entities:  

Keywords:  Achondroplasia; Acromegaly; Cartilage–hair hypoplasia; Ellis–van Creveld syndrome; Fibrodysplasia ossificans progressiva; Kniest dysplasia; Marfan syndrome; Mucopolysaccharidosis; Nail–patella syndrome; Pseudohypoparathyroidism

Year:  2010        PMID: 22379434      PMCID: PMC3041879          DOI: 10.1007/s11552-010-9302-8

Source DB:  PubMed          Journal:  Hand (N Y)        ISSN: 1558-9447


  83 in total

1.  Ellis-van Creveld syndrome and the Amish.

Authors:  V A McKusick
Journal:  Nat Genet       Date:  2000-03       Impact factor: 38.330

2.  The Kniest syndrome.

Authors:  R S Lachman; D L Rimoin; D W Hollister; J P Dorst; D C Siggers; W McAlister; R L Kaufman; L O Langer
Journal:  Am J Roentgenol Radium Ther Nucl Med       Date:  1975-04

3.  Bilateral accessory iliac horns: pathognomonic findings in Nail-patella syndrome. Scintigraphic evidence on bone scan.

Authors:  E Goshen; A Schwartz; L R Zilka; S T Zwas
Journal:  Clin Nucl Med       Date:  2000-06       Impact factor: 7.794

4.  Disordered breathing during sleep in patients with mucopolysaccharidoses.

Authors:  S E Leighton; B Papsin; A Vellodi; R Dinwiddie; R Lane
Journal:  Int J Pediatr Otorhinolaryngol       Date:  2001-04-27       Impact factor: 1.675

5.  Ellis-van Creveld syndrome: a generalized dysplasia of enchondral ossification.

Authors:  C Sergi; T Voigtländer; S Zoubaa; S Hentze; G Meyberg-Solomeyer; J Troeger; G Tariverdian; H F Otto; M Schiesser
Journal:  Pediatr Radiol       Date:  2001-04

6.  Dural ectasia is associated with back pain in Marfan syndrome.

Authors:  N U Ahn; P D Sponseller; U M Ahn; L Nallamshetty; B S Kuszyk; S J Zinreich
Journal:  Spine (Phila Pa 1976)       Date:  2000-06-15       Impact factor: 3.468

7.  Radiologic changes in infancy in McKusick cartilage hair hypoplasia.

Authors:  R B Glass; C J Tifft
Journal:  Am J Med Genet       Date:  1999-10-08

8.  RMRP gene sequence analysis confirms a cartilage-hair hypoplasia variant with only skeletal manifestations and reveals a high density of single-nucleotide polymorphisms.

Authors:  L Bonafé; K Schmitt; G Eich; A Giedion; A Superti-Furga
Journal:  Clin Genet       Date:  2002-02       Impact factor: 4.438

9.  Worldwide mutation spectrum in cartilage-hair hypoplasia: ancient founder origin of the major70A-->G mutation of the untranslated RMRP.

Authors:  Maaret Ridanpää; Pertti Sistonen; Susanna Rockas; David L Rimoin; Outi Mäkitie; Ilkka Kaitila
Journal:  Eur J Hum Genet       Date:  2002-07       Impact factor: 4.246

10.  Airway changes in children with mucopolysaccharidoses.

Authors:  Shin-Lin Shih; Y-J Lee; S-P Lin; C-Y Sheu; J G Blickman
Journal:  Acta Radiol       Date:  2002-01       Impact factor: 1.701

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  5 in total

Review 1.  Radiographic assessment of congenital malformations of the upper extremity.

Authors:  Matthew J Winfeld; Hansel Otero
Journal:  Pediatr Radiol       Date:  2016-06-15

Review 2.  Hand X-ray in pediatric endocrinology: Skeletal age assessment and beyond.

Authors:  Vincenzo De Sanctis; Salvatore Di Maio; Ashraf T Soliman; Giuseppe Raiola; Rania Elalaily; Giuseppe Millimaggi
Journal:  Indian J Endocrinol Metab       Date:  2014-11

3.  First applications of a targeted exome sequencing approach in fetuses with ultrasound abnormalities reveals an important fraction of cases with associated gene defects.

Authors:  Constantinos Pangalos; Birgitta Hagnefelt; Konstantinos Lilakos; Christopher Konialis
Journal:  PeerJ       Date:  2016-04-26       Impact factor: 2.984

4.  Imaging findings of mucopolysaccharidoses: a pictorial review.

Authors:  Stefano Palmucci; Giancarlo Attinà; Maria Letizia Lanza; Giuseppe Belfiore; Giuseppina Cappello; Pietro Valerio Foti; Pietro Milone; Domenico Di Bella; Rita Barone; Agata Fiumara; Giovanni Sorge; Giovanni Carlo Ettorre
Journal:  Insights Imaging       Date:  2013-05-05

5.  Multiple impacted Permanent Teeth-An Indicator for Early Detection of Hypoparathyroidism: A Rare Case Report.

Authors:  B Suresh Babu; Thatapudi A Shankar; Moon Chattaraj; K Kongkana; S Venugopal; Abhishek Singh Nayyar
Journal:  Indian J Endocrinol Metab       Date:  2018 Sep-Oct
  5 in total

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