A continent urinary diversion in a female with agenesis of the bladder: a 5-year follow-up.

There are few case reports of bladder agenesis. The outcome of the patients differs and depends on the associated malformations. Different urinary diversions are described to save renal function. Most of the surviving patients with bladder agenesis have undergone incontinent urinary diversions as primary treatment. We describe the case of a female infant with agenesis of the bladder that arrived in our institution after several septic episodes. Treatment of choice was a continent pouch with an appendicovesicostomy. We state that even in young children, a primary continent urinary diversion can be performed with excellent long-term outcome.