Literature DB >> 22159065

Ultrastructural mitochondrial abnormalities in patients with sporadic amyotrophic lateral sclerosis.

Laura Napoli, Veronica Crugnola, Costanza Lamperti, Vincenzo Silani, Salvatore Di Mauro, Nereo Bresolin, Maurizio Moggio.   

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Year:  2011        PMID: 22159065     DOI: 10.1001/archneur.68.12.1612

Source DB:  PubMed          Journal:  Arch Neurol        ISSN: 0003-9942


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  9 in total

1.  ROS-related mitochondrial dysfunction in skeletal muscle of an ALS mouse model during the disease progression.

Authors:  Yajuan Xiao; Chehade Karam; Jianxun Yi; Lin Zhang; Xuejun Li; Dosuk Yoon; Huan Wang; Kamal Dhakal; Paul Ramlow; Tian Yu; Zhaohui Mo; Jianjie Ma; Jingsong Zhou
Journal:  Pharmacol Res       Date:  2018-09-18       Impact factor: 7.658

2.  Peculiar histological and ultrastructural skeletal muscle alterations in a patient with CMV infection and autoimmune myositis: case evaluation and brief literature review.

Authors:  Michela Ripolone; Laura Napoli; Vittorio Mantero; Monica Sciacco; Simona Zanotti
Journal:  Acta Myol       Date:  2022-03-31

Review 3.  Dysregulated mitochondrial Ca2+ and ROS signaling in skeletal muscle of ALS mouse model.

Authors:  Jingsong Zhou; Ang Li; Xuejun Li; Jianxun Yi
Journal:  Arch Biochem Biophys       Date:  2019-01-22       Impact factor: 4.013

4.  Molecular signatures of amyotrophic lateral sclerosis disease progression in hind and forelimb muscles of an SOD1(G93A) mouse model.

Authors:  Daniele Capitanio; Michele Vasso; Antonia Ratti; Giuliano Grignaschi; Manuela Volta; Manuela Moriggi; Cristina Daleno; Caterina Bendotti; Vincenzo Silani; Cecilia Gelfi
Journal:  Antioxid Redox Signal       Date:  2012-06-13       Impact factor: 8.401

5.  Pantethine treatment is effective in recovering the disease phenotype induced by ketogenic diet in a pantothenate kinase-associated neurodegeneration mouse model.

Authors:  Dario Brunetti; Sabrina Dusi; Carla Giordano; Costanza Lamperti; Michela Morbin; Valeria Fugnanesi; Silvia Marchet; Gigliola Fagiolari; Ody Sibon; Maurizio Moggio; Giulia d'Amati; Valeria Tiranti
Journal:  Brain       Date:  2013-12-06       Impact factor: 13.501

6.  MG53 Preserves Neuromuscular Junction Integrity and Alleviates ALS Disease Progression.

Authors:  Jianxun Yi; Ang Li; Xuejun Li; Kiho Park; Xinyu Zhou; Frank Yi; Yajuan Xiao; Dosuk Yoon; Tao Tan; Lyle W Ostrow; Jianjie Ma; Jingsong Zhou
Journal:  Antioxidants (Basel)       Date:  2021-09-25

7.  Butyrate Ameliorates Mitochondrial Respiratory Capacity of The Motor-Neuron-like Cell Line NSC34-G93A, a Cellular Model for ALS.

Authors:  Xuejun Li; Li Dong; Ang Li; Jianxun Yi; Marco Brotto; Jingsong Zhou
Journal:  Biomolecules       Date:  2022-02-19

Review 8.  Amyotrophic Lateral Sclerosis and Autophagy: Dysfunction and Therapeutic Targeting.

Authors:  Azin Amin; Nirma D Perera; Philip M Beart; Bradley J Turner; Fazel Shabanpoor
Journal:  Cells       Date:  2020-11-04       Impact factor: 6.600

Review 9.  Autophagy and ALS: mechanistic insights and therapeutic implications.

Authors:  Jason P Chua; Hortense De Calbiac; Edor Kabashi; Sami J Barmada
Journal:  Autophagy       Date:  2021-05-31       Impact factor: 16.016

  9 in total

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