| Literature DB >> 2206977 |
P C van de Kerkhof1, C M Weemaes.
Abstract
In congenital deficiency of leucocyte-adherence glycoproteins (CDLG) there is an immunodeficiency with impaired leucocyte function and cutaneous and extracutaneous infections occur. In more than 30% of cases the condition has a fatal course. We report the skin manifestations of three siblings with CDLG in which areas of skin necrosis occurred that resembled pyoderma gangrenosum.Entities:
Mesh：
Year: 1990 PMID： 2206977 DOI： 10.1111/j.1365-2133.1990.tb06301.x
Source DB: PubMed Journal: Br J Dermatol ISSN： 0007-0963 Impact factor: 9.302