Literature DB >> 22045111

Massive bilateral renal angiomyolipomatosis and multifocal micronodular pneumocytes hyperplasia associated with tuberous sclerosis: a case report.

Mehmet Incedayi1, Guner Sonmez, Cinar Basekim.   

Abstract

Tuberous sclerosis (TS) is an autosomal-dominant disorder characterized by a variety of hamartomatous lesions in various organs. Various organ involvements can be detected with radiology: neurologic involvement (cortical tubers, subependymal nodules and white matter abnormalities), renal involvement (angiomyolipoma) and pulmonary involvement (pulmonary lymphangioleiomyomatosis, multifocal micronodular pneumocyte hyperplasia). Here, we are reporting a case of tuberous sclerosis with multiple organ involvement and massive bilateral AMLs in a 49-year-old female patient.

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Year:  2011        PMID: 22045111     DOI: 10.1007/s00508-011-0073-1

Source DB:  PubMed          Journal:  Wien Klin Wochenschr        ISSN: 0043-5325            Impact factor:   1.704


  13 in total

1.  US case of the day. Large, bilateral angiomyolipomas of the kidneys with tuberous sclerosis.

Authors:  T C Carter; T L Angtuaco; H R Shah
Journal:  Radiographics       Date:  1999 Mar-Apr       Impact factor: 5.333

2.  Bilateral massive renal angiomyolipomatosis in tuberous sclerosis.

Authors:  Howard Liu; Kenneth Cooke; David Frager
Journal:  AJR Am J Roentgenol       Date:  2005-10       Impact factor: 3.959

3.  Unusual fat-containing tumors of the kidney: a diagnostic dilemma.

Authors:  O Hélénon; S Merran; F Paraf; P Melki; J M Correas; Y Chrétien; J F Moreau
Journal:  Radiographics       Date:  1997 Jan-Feb       Impact factor: 5.333

Review 4.  CT and MR imaging of extrahepatic fatty masses of the abdomen and pelvis: techniques, diagnosis, differential diagnosis, and pitfalls.

Authors:  Jose M Pereira; Claude B Sirlin; Pedro S Pinto; Giovanna Casola
Journal:  Radiographics       Date:  2005 Jan-Feb       Impact factor: 5.333

5.  Concurrent bilateral renal angiomyolipoma and renal cell carcinoma in a patient with tuberous sclerosis complex.

Authors:  Abdelhak Khallouk; Younes Ahallal; Mbarek Doublali; Mohamed Fadl Tazi; Soufiane Mellas; Mohamed Jamal El Fassi; Moulay Hassan Farih
Journal:  Rev Urol       Date:  2009

6.  Giant angiomyolipoma associated with marked pulmonary lesions suggesting lymphangioleiomyomatosis in a patient with tuberous sclerosis.

Authors:  E Tüzel; Z Kirkali; U Mungan; C Cüler; M Sade
Journal:  Int Urol Nephrol       Date:  2000       Impact factor: 2.370

7.  Mutational and radiographic analysis of pulmonary disease consistent with lymphangioleiomyomatosis and micronodular pneumocyte hyperplasia in women with tuberous sclerosis.

Authors:  D N Franz; A Brody; C Meyer; J Leonard; G Chuck; S Dabora; G Sethuraman; T V Colby; D J Kwiatkowski; F X McCormack
Journal:  Am J Respir Crit Care Med       Date:  2001-08-15       Impact factor: 21.405

8.  Endovascular therapy for patients with renal angiomyolipoma presenting with retroperitoneal haemorrhage.

Authors:  M Incedayi; U C Turba; B Arslan; S S Sabri; W E A Saad; A H Matsumoto; J F Angle
Journal:  Eur J Vasc Endovasc Surg       Date:  2010-01-21       Impact factor: 7.069

9.  Multifocal micronodular pneumocyte hyperplasia associated with tuberous sclerosis: differentiation from multiple atypical adenomatous hyperplasia.

Authors:  Yoshihiro Kobashi; Tadaaki Sugiu; Keiji Mouri; Tsutomu Irei; Masao Nakata; Mikio Oka
Journal:  Jpn J Clin Oncol       Date:  2008-06-05       Impact factor: 3.019

Review 10.  Pictorial review of tuberous sclerosis in various organs.

Authors:  Shigeaki Umeoka; Takashi Koyama; Yukio Miki; Mikio Akai; Kazushige Tsutsui; Kaori Togashi
Journal:  Radiographics       Date:  2008-09-04       Impact factor: 5.333

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  2 in total

1.  Spontaneous rupture of angiomyolipoma of the kidney.

Authors:  Friedrich C Prischl; Peter Spöttl
Journal:  Wien Klin Wochenschr       Date:  2017-02-10       Impact factor: 1.704

2.  Malignant renal angiomyolipoma without tuberous sclerosis.

Authors:  Antonio Cusano; Fernando Abarzua-Cabezas; Anoop Meraney
Journal:  BMJ Case Rep       Date:  2014-04-30
  2 in total

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