Protein-losing enteropathy resolved by percutaneous intervention.

The extracardiac total cavopulmonary connection is the final stage of palliation of hearts with single-ventricle physiology. Protein-losing enteropathy (PLE) and plastic bronchitis are catastrophic sequale that may occur in patients with the total cavopulmonary connection and may complicate the early and long-term follow-up. Here we report on the successful treatment of a 16-year boy affected by PLE by percutaneous closure of a persistent anterograde pulmonary blood flow by using an 8-mm Amplatzer VSD Occluder.