| Literature DB >> 21738992 |
Isabella Brasil Succi1, Fernando Colonna Rosman, Elisa Fontenelle de Oliveira.
Abstract
Bloch-Sulzberger syndrome (incontinentia pigmenti) is a rare genodermatosis that affects predominantly females, since it is generally lethal to male fetuses in utero. It is characterized principally by skin lesions, but may also involve dental, ophthalmological and neurological abnormalities. The skin lesions are present in four different phases: vesicular, verrucous, hyperpigmented and atrophic/hypopigmented. Their sequence is irregular and overlapping of stages is common.Entities:
Mesh:
Year: 2011 PMID: 21738992 DOI: 10.1590/s0365-05962011000300037
Source DB: PubMed Journal: An Bras Dermatol ISSN: 0365-0596 Impact factor: 1.896