Literature DB >> 21607045

Atypical hemolytic-uremic syndrome (HUS) with recovery after a long-lasting anuria: a case report.

H Georgaki-Angelaki, N Stergiou, A Kapogiannis, I Orfanou, B Grapsa, E Roma.   

Abstract

We report a case of a seven-year-old girl who suffered from atypical Hemolytic Uremic Syndrome (aHUS) complicated by septicaemia, central nervous system involvement, and cholangiitis. She remained anuric requiring treatment with peritoneal dialysis (PD) for a five-month period. In addition to conventional therapeutic measures including fresh frozen plasma (FFP) and blood cells transfusions she also underwent to plasma exchange (PE) treatment. Following a stormy hospitalization period of 17 weeks, the patient finally regained renal function and three years later she remains well on antihypertensive treatment and free of dialysis.

Entities:  

Keywords:  anuria; atypical Hemolytic Uremic Syndrome; cholangitis; seizures

Year:  2011        PMID： 21607045      PMCID： PMC3093155     

Source DB:  PubMed          Journal:  Hippokratia        ISSN： 1108-4189            Impact factor:   0.471


  16 in total

Review 1.  Atypical haemolytic uraemic syndrome and mutations in complement regulator genes.

Authors:  Marie-Agnès Dragon-Durey; Véronique Frémeaux-Bacchi
Journal:  Springer Semin Immunopathol       Date:  2005-11-11

Review 2.  Typical and atypical hemolytic uremic syndrome.

Authors:  W Proesmans
Journal:  Kidney Blood Press Res       Date:  1996       Impact factor: 2.687

Review 3.  Thrombotic microangiopathy, hemolytic uremic syndrome, and thrombotic thrombocytopenic purpura.

Authors:  P Ruggenenti; M Noris; G Remuzzi
Journal:  Kidney Int       Date:  2001-09       Impact factor: 10.612

Review 4.  Pathophysiology and management of thrombotic microangiopathies.

Authors:  P Ruggenenti; G Remuzzi
Journal:  J Nephrol       Date:  1998 Nov-Dec       Impact factor: 3.902

5.  Atypical (non-diarrhea-associated) hemolytic-uremic syndrome in childhood.

Authors:  M M Fitzpatrick; M D Walters; R S Trompeter; M J Dillon; T M Barratt
Journal:  J Pediatr       Date:  1993-04       Impact factor: 4.406

6.  Outcome and prognostic determinants in the hemolytic uremic syndrome of children.

Authors:  B Tönshoff; A Sammet; I Sanden; O Mehls; R Waldherr; K Schärer
Journal:  Nephron       Date:  1994       Impact factor: 2.847

7.  Plasma exchange in children with hemolytic-uremic syndrome at risk of poor outcome.

Authors:  A Gianviti; A Perna; A Caringella; A Edefonti; R Penza; G Remuzzi; G Rizzoni
Journal:  Am J Kidney Dis       Date:  1993-08       Impact factor: 8.860

8.  Haemolytic uraemic syndrome and mutations of the factor H gene: a registry-based study of German speaking countries.

Authors:  H P H Neumann; M Salzmann; B Bohnert-Iwan; T Mannuelian; C Skerka; D Lenk; B U Bender; M Cybulla; P Riegler; A Königsrainer; U Neyer; A Bock; U Widmer; D A Male; G Franke; P F Zipfel
Journal:  J Med Genet       Date:  2003-09       Impact factor: 6.318

9.  Long-term follow-up of Argentinean patients with hemolytic uremic syndrome who had not undergone dialysis.

Authors:  Carlos J Cobeñas; Laura F Alconcher; Ana P Spizzirri; Ricardo C Rahman
Journal:  Pediatr Nephrol       Date:  2007-06-13       Impact factor: 3.714

10.  Haemolytic-uraemic syndrome: an analysis of prognostic features.

Authors:  R S Trompeter; R Schwartz; C Chantler; M J Dillon; G B Haycock; R Kay; T M Barratt
Journal:  Arch Dis Child       Date:  1983-02       Impact factor: 3.791
View more
  2 in total

1.  Recovery of renal function in a heart transplantation recipient with over 300 days of iatrogenic anuria: A case report.

Authors:  Yong-Hua Peng; Xiao-Min Yu; Chen Yan; Lan Luo; Tao-Sheng Li; Jie Xiao
Journal:  Medicine (Baltimore)       Date:  2018-04       Impact factor: 1.889

2.  End-stage kidney disease due to haemolytic uraemic syndrome--outcomes in 241 consecutive ANZDATA registry cases.

Authors:  Wen Tang; Janaki Mohandas; Stephen P McDonald; Carmel M Hawley; Sunil V Badve; Neil Boudville; Fiona G Brown; Philip A Clayton; Kathryn J Wiggins; Kym M Bannister; Scott B Campbell; David W Johnson
Journal:  BMC Nephrol       Date:  2012-12-03       Impact factor: 2.388
  2 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.