Divya K Shah1, Marc R Laufer. 1. Division of Reproductive Endocrinology and Infertility, Department of Obstetrics and Gynecology, Brigham and Women's Hospital, Boston, Massachusetts, USA.
Abstract
OBJECTIVE: To describe an unusual case of obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome with a single uterus. DESIGN: Case report. SETTING: Major academic medical center. PATIENT(S): A 12-year-old girl with OHVIRA syndrome. INTERVENTION(S): None. MAIN OUTCOME MEASURE(S): None. RESULT(S): A 12-year-old girl presented with presumed OHVIRA syndrome and had surgical correction of the obstructed hemivagina. Two years later she presented with increasing pelvic pain and underwent laparoscopy for presumed endometriosis. A single uterus with a broad flat fundus was found as well as endometriosis. CONCLUSION(S): OHVIRA syndrome is typically associated with a didelphys uterus with two cervices and two vaginas, one of which is obstructed. The obstruction usually occurs on the same side as the renal anomaly. We report a rare congenital anomaly of the female reproductive tract: OHVIRA syndrome with a single uterus. From a fertility standpoint, cases of a single uterus with two cervices are managed differently than two uteri with two cervices. Healthcare providers managing complex reproductive tract anomalies should be aware of this potential variant.
OBJECTIVE: To describe an unusual case of obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome with a single uterus. DESIGN: Case report. SETTING: Major academic medical center. PATIENT(S): A 12-year-old girl with OHVIRA syndrome. INTERVENTION(S): None. MAIN OUTCOME MEASURE(S): None. RESULT(S): A 12-year-old girl presented with presumed OHVIRA syndrome and had surgical correction of the obstructed hemivagina. Two years later she presented with increasing pelvic pain and underwent laparoscopy for presumed endometriosis. A single uterus with a broad flat fundus was found as well as endometriosis. CONCLUSION(S): OHVIRA syndrome is typically associated with a didelphys uterus with two cervices and two vaginas, one of which is obstructed. The obstruction usually occurs on the same side as the renal anomaly. We report a rare congenital anomaly of the female reproductive tract: OHVIRA syndrome with a single uterus. From a fertility standpoint, cases of a single uterus with two cervices are managed differently than two uteri with two cervices. Healthcare providers managing complex reproductive tract anomalies should be aware of this potential variant.
Authors: Riccardo Del Vescovo; Sofia Battisti; Valerio Di Paola; Claudia L Piccolo; Roberto L Cazzato; Ilaria Sansoni; Rosario F Grasso; Bruno Beomonte Zobel Journal: BMC Med Imaging Date: 2012-03-09 Impact factor: 1.930
Authors: A Di Spiezio Sardo; R Campo; S Gordts; M Spinelli; C Cosimato; V Tanos; S Brucker; T C Li; M Gergolet; C De Angelis; L Gianaroli; G Grimbizis Journal: Hum Reprod Date: 2015-03-18 Impact factor: 6.918