OBJECTIVE: Paragangliomas of the sella are rare; 14 cases have been reported in the literature. We describe here the unique case of a sellar paraganglioma that extended into the orbit through the superior orbital fissure. We have also reviewed all reported cases of sellar paragangliomas to better define best management strategies. CLINICAL PRESENTATION: A 63-year-old male presented with left eye proptosis and conjunctival vessel dilatation. INTERVENTION: Resection of the intraorbital component of the tumor was accomplished using a transcranial-transorbital approach. CONCLUSION: This is the first report of a sellar/parasellar paraganglioma extending into the orbit through the superior orbital fissure. While an appropriate treatment paradigm has not been established, a review of all previously reported cases suggests that radiotherapy is an important consideration.
OBJECTIVE: Paragangliomas of the sella are rare; 14 cases have been reported in the literature. We describe here the unique case of a sellar paraganglioma that extended into the orbit through the superior orbital fissure. We have also reviewed all reported cases of sellar paragangliomas to better define best management strategies. CLINICAL PRESENTATION: A 63-year-old male presented with left eye proptosis and conjunctival vessel dilatation. INTERVENTION: Resection of the intraorbital component of the tumor was accomplished using a transcranial-transorbital approach. CONCLUSION: This is the first report of a sellar/parasellar paraganglioma extending into the orbit through the superior orbital fissure. While an appropriate treatment paradigm has not been established, a review of all previously reported cases suggests that radiotherapy is an important consideration.
Authors: Jacob Ruzevick; Eun Kyung Koh; Luis F Gonzalez-Cuyar; Patrick J Cimino; Kristen Moe; Lorena A Wright; Richard Failor; Manuel Ferreira Journal: J Neurooncol Date: 2017-03-16 Impact factor: 4.130