Literature DB >> 21423479

Coronary artery bypass surgery in a patient with analbuminemia.

Ergun Demirsoy1, Gokce Sirin, Emre Ozker.   

Abstract

Congenital analbuminemia is a rare autosomal recessive disorder characterized by the absence of serum albumin, or by its presence in very low concentrations. Up to now, only 43 cases have been reported. There is little information about analbuminemia, and no operation on an analbuminemic patient has been reported. This, we believe, is the 1st report of an operation on an analbuminemic patient for coronary artery disease in which the perioperative experience is presented.

Entities:  

Keywords:  Albumins/deficiency/genetics; blood proteins; coronary artery bypass grafting; risk factor; serum albumin/analysis/deficiency/genetics

Mesh:

Substances:

Year:  2011        PMID: 21423479      PMCID: PMC3060746     

Source DB:  PubMed          Journal:  Tex Heart Inst J        ISSN: 0730-2347


  7 in total

Review 1.  [A further case of analbuminemia].

Authors:  B Gössi; D Kleinert; U Gössi
Journal:  Schweiz Med Wochenschr       Date:  2000-04-22

Review 2.  Congenital analbuminaemia: biochemical and clinical implications. A case report and literature review.

Authors:  Bart G P Koot; Roderick Houwen; Dirk-Jan Pot; Jeroen Nauta
Journal:  Eur J Pediatr       Date:  2004-08-06       Impact factor: 3.183

3.  Congenital analbuminemia attributable to compound heterozygosity for novel mutations in the albumin gene.

Authors:  Filomena Campagna; Francesca Fioretti; Marco Burattin; Stefano Romeo; Federica Sentinelli; Maura Bifolco; Maria Isabella Sirinian; Maria Del Ben; Francesco Angelico; Marcello Arca
Journal:  Clin Chem       Date:  2005-07       Impact factor: 8.327

4.  The use of simvastatin in analbuminaemia.

Authors:  L J Burgess; A D Marais
Journal:  Cardiovasc Drugs Ther       Date:  2001-11       Impact factor: 3.727

5.  Turnover of autologous alpha 1-antitrypsin in a patient with congenital analbuminemia.

Authors:  K Weigand; E Russi; G von Schulthess; C Bavaud
Journal:  Klin Wochenschr       Date:  1983-06-01

6.  Molecular diagnosis of analbuminemia: a novel mutation identified in two Amerindian and two Turkish families.

Authors:  Monica Galliano; Monica Campagnoli; Antonio Rossi; Carl Heinz Wirsing von König; Andrew W Lyon; Kivanc Cefle; Alaattin Yildiz; Sukru Palanduz; Sukru Ozturk; Lorenzo Minchiotti
Journal:  Clin Chem       Date:  2002-06       Impact factor: 8.327

7.  Further studies on plasma proteins, lipids, and dye- and drug-binding in a child with analbuminemia.

Authors:  J Frohlich; M R Pudek; E J Cormode; E M Sellers; J G Abel
Journal:  Clin Chem       Date:  1981-07       Impact factor: 8.327

  7 in total
  5 in total

1.  Pregnancy in a patient with congenital analbuminaemia.

Authors:  Hillary Hu; Roshini Nayyar; Lucinda Jean Berglund; Elizabeth Anne Anderson
Journal:  BMJ Case Rep       Date:  2017-02-02

2.  Treatment of a patient with congenital analbuminemia with atorvastatin and albumin infusion.

Authors:  Maria Del Ben; Francesco Angelico; Lorenzo Loffredo; Francesco Violi
Journal:  World J Clin Cases       Date:  2013-04-16       Impact factor: 1.337

3.  Congenital analbuminemia in a patient affected by hypercholesterolemia: A case report.

Authors:  Patrizia Suppressa; Concetta Carbonara; Francesca Lugani; Monica Campagnoli; Teresa Troiano; Lorenzo Minchiotti; Carlo Sabbà
Journal:  World J Clin Cases       Date:  2019-02-26       Impact factor: 1.337

4.  A nucleotide deletion and frame-shift cause analbuminemia in a Turkish family.

Authors:  Gianluca Caridi; Elif Yilmaz Gulec; Monica Campagnoli; Francesca Lugani; Hasan Onal; Duzgun Kilic; Monica Galliano; Lorenzo Minchiotti
Journal:  Biochem Med (Zagreb)       Date:  2016       Impact factor: 2.313

Review 5.  Diagnosis, Phenotype, and Molecular Genetics of Congenital Analbuminemia.

Authors:  Lorenzo Minchiotti; Gianluca Caridi; Monica Campagnoli; Francesca Lugani; Monica Galliano; Ulrich Kragh-Hansen
Journal:  Front Genet       Date:  2019-04-17       Impact factor: 4.599

  5 in total

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