Intracranial rosai-dorfman: a clinical challenge.

Rosai-Dorfman disease has been described as massive painless cervical lymphadenopathy with a benign clinical course and unclear etiology. Isolated extranodal involvement has been rarely described. We present a rare case of isolated intracranial Rosai-Dorfman disease that was diagnosed and treated at our institution. Our diagnostic and clinical challenges are presented with a review of the literature.