| Literature DB >> 21133995 |
Marta Gutiérrez-Pascual1, Angela Hernández-Martín, Isabel Colmenero, Juan José García-Peñas, Miguel Angel López-Pino, Antonio Torrelo.
Abstract
Malignant atrophic papulosis, or Degos' disease, is a severe systemic vasculopathy extremely rare in children. The skin, gastrointestinal tract, and central nervous system are most frequently affected. We report a 5-year-old girl with malignant atrophic papulosis who presented with widespread skin lesions from early infancy and severe visual and neurological impairment.Entities:
Mesh:
Year: 2010 PMID: 21133995 DOI: 10.1111/j.1525-1470.2010.01287.x
Source DB: PubMed Journal: Pediatr Dermatol ISSN: 0736-8046 Impact factor: 1.588