Literature DB >> 21110275

Early surgical management of chylothorax complicated by Gorham's disease.

Y K Seok1, S Cho, E Lee.   

Abstract

Gorham's disease is a rare disorder and its etiology remains unknown. It is characterized by the proliferation of vascular structures in bone, and results in progressive osteolysis. Chylothorax is a severe complication of Gorham's disease with a mortality of 50%. We report a 14-year-old boy with Gorham's disease complicated by chylothorax who underwent early surgical management followed by radiotherapy. © Georg Thieme Verlag KG Stuttgart · New York.

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Year:  2010        PMID: 21110275     DOI: 10.1055/s-0030-1250158

Source DB:  PubMed          Journal:  Thorac Cardiovasc Surg        ISSN: 0171-6425            Impact factor:   1.827


  4 in total

1.  Efficacy of systemic sirolimus in the treatment of generalized lymphatic anomaly and Gorham-Stout disease.

Authors:  Kiersten W Ricci; Adrienne M Hammill; Paula Mobberley-Schuman; Stephen C Nelson; Julie Blatt; Julia L Glade Bender; Catherine C McCuaig; Anna Synakiewicz; Ilona J Frieden; Denise M Adams
Journal:  Pediatr Blood Cancer       Date:  2019-01-22       Impact factor: 3.167

2.  Japanese clinical practice guidelines for vascular anomalies 2017.

Authors:  Hidefumi Mimura; Sadanori Akita; Akihiro Fujino; Masatoshi Jinnin; Mine Ozaki; Keigo Osuga; Hiroki Nakaoka; Eiichi Morii; Akira Kuramochi; Yoko Aoki; Yasunori Arai; Noriko Aramaki; Masanori Inoue; Yuki Iwashina; Tadashi Iwanaka; Shigeru Ueno; Akihiro Umezawa; Michio Ozeki; Junko Ochi; Yoshiaki Kinoshita; Masakazu Kurita; Shien Seike; Nobuyuki Takakura; Masataka Takahashi; Takao Tachibana; Kumiko Chuman; Shuji Nagata; Mitsunaga Narushima; Yasunari Niimi; Shunsuke Nosaka; Taiki Nozaki; Kazuki Hashimoto; Ayato Hayashi; Satoshi Hirakawa; Atsuko Fujikawa; Yumiko Hori; Kentaro Matsuoka; Hideki Mori; Yuki Yamamoto; Shunsuke Yuzuriha; Naoaki Rikihisa; Shoji Watanabe; Shinichi Watanabe; Tatsuo Kuroda; Shunsuke Sugawara; Kosuke Ishikawa; Satoru Sasaki
Journal:  Jpn J Radiol       Date:  2020-04       Impact factor: 2.374

3.  Japanese Clinical Practice Guidelines for Vascular Anomalies 2017.

Authors:  Hidefumi Mimura; Sadanori Akita; Akihiro Fujino; Masatoshi Jinnin; Mine Ozaki; Keigo Osuga; Hiroki Nakaoka; Eiichi Morii; Akira Kuramochi; Yoko Aoki; Yasunori Arai; Noriko Aramaki; Masanori Inoue; Yuki Iwashina; Tadashi Iwanaka; Shigeru Ueno; Akihiro Umezawa; Michio Ozeki; Junko Ochi; Yoshiaki Kinoshita; Masakazu Kurita; Shien Seike; Nobuyuki Takakura; Masataka Takahashi; Takao Tachibana; Kumiko Chuman; Shuji Nagata; Mitsunaga Narushima; Yasunari Niimi; Shunsuke Nosaka; Taiki Nozaki; Kazuki Hashimoto; Ayato Hayashi; Satoshi Hirakawa; Atsuko Fujikawa; Yumiko Hori; Kentaro Matsuoka; Hideki Mori; Yuki Yamamoto; Shunsuke Yuzuriha; Naoaki Rikihisa; Shoji Watanabe; Shinichi Watanabe; Tatsuo Kuroda; Shunsuke Sugawara; Kosuke Ishikawa; Satoru Sasaki
Journal:  J Dermatol       Date:  2020-03-22       Impact factor: 4.005

4.  Gastrointestinal Tract Involvement of Gorham's Disease with Expression of D2-40 in Duodenum.

Authors:  Bong Seok Choi; Suk Jin Hong; Mi Ae Chu; Seok Jong Lee; Jong-Min Lee; Han Ik Bae; Byung-Ho Choe
Journal:  Pediatr Gastroenterol Hepatol Nutr       Date:  2014-03-31
  4 in total

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