Literature DB >> 21046409

Variably protease-sensitive prionopathy in a PRNP codon 129 heterozygous UK patient with co-existing tau, α synuclein and Aβ pathology.

Mark W Head, Suzanne Lowrie, Gurjit Chohan, Richard Knight, David J Scoones, James W Ironside.   

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Year:  2010        PMID： 21046409     DOI： 10.1007/s00401-010-0766-y

Source DB:  PubMed          Journal:  Acta Neuropathol        ISSN： 0001-6322            Impact factor:   17.088


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  16 in total

1.  Variably Protease-sensitive Prionopathy in an Apparent Cognitively Normal 93-Year-Old.

Authors:  Nupur Ghoshal; Arie Perry; Daniel McKeel; Robert E Schmidt; Deborah Carter; Joanne Norton; Wen-Quan Zou; Xiangzhu Xiao; Gianfranco Puoti; Silvio Notari; Pierluigi Gambetti; John C Morris; Nigel J Cairns
Journal:  Alzheimer Dis Assoc Disord       Date:  2015 Apr-Jun       Impact factor: 2.703

2.  Concurrent variably protease-sensitive prionopathy and amyotrophic lateral sclerosis.

Authors:  Ashley Cannon; Kevin F Bieniek; Wen-Lang Lin; Silvio Notari; Wen-Quan Zou; Pierluigi Gambetti; Otto Pedraza; Neill R Graff-Radford; Tanis J Ferman; Dennis W Dickson
Journal:  Acta Neuropathol       Date:  2014-06-14       Impact factor: 17.088

3.  Prion infection promotes extensive accumulation of α-synuclein in aged human α-synuclein transgenic mice.

Authors:  Eliezer Masliah; Edward Rockenstein; Chandra Inglis; Anthony Adame; Cyrus Bett; Melanie Lucero; Christina J Sigurdson
Journal:  Prion       Date:  2012-04-01       Impact factor: 3.931

4.  Variably protease-sensitive prionopathy: a novel disease of the prion protein.

Authors:  Pierluigi Gambetti; Gianfranco Puoti; Wen-Quan Zou
Journal:  J Mol Neurosci       Date:  2011-05-17       Impact factor: 3.444

5.  Further Characterization of Glycoform-Selective Prions of Variably Protease-Sensitive Prionopathy.

Authors:  Weiguanliu Zhang; Xiangzhu Xiao; Mingxuan Ding; Jue Yuan; Aaron Foutz; Mohammed Moudjou; Tetsuyuki Kitamoto; Jan P M Langeveld; Li Cui; Wen-Quan Zou
Journal:  Pathogens       Date:  2021-04-23

6.  Coexistence of protease sensitive and resistant prion protein in 129VV homozygous sporadic Creutzfeldt-Jakob disease: a case report.

Authors:  Ana B Rodríguez-Martínez; Adolfo López de Munain; Isidro Ferrer; Juan J Zarranz; Begoña Atarés; Nuria T Villagra; Jose M Arteagoitia; Joseba M Garrido; Ramón A Juste
Journal:  J Med Case Rep       Date:  2012-10-11

7.  Variably Protease-sensitive Prionopathy in a Middle-aged Man With Rapidly Progressive Dementia.

Authors:  Juebin Huang; Mark Cohen; Jiri Safar; Alexander P Auchus
Journal:  Cogn Behav Neurol       Date:  2021-09-02       Impact factor: 1.590

8.  Classification of diseases with accumulation of Tau protein.

Authors:  Gabor G Kovacs; Bernardino Ghetti; Michel Goedert
Journal:  Neuropathol Appl Neurobiol       Date:  2022-02-09       Impact factor: 6.250

Review 9.  Prion protein misfolding, strains, and neurotoxicity: an update from studies on Mammalian prions.

Authors:  Ilaria Poggiolini; Daniela Saverioni; Piero Parchi
Journal:  Int J Cell Biol       Date:  2013-12-24

10.  The prion protein protease sensitivity, stability and seeding activity in variably protease sensitive prionopathy brain tissue suggests molecular overlaps with sporadic Creutzfeldt-Jakob disease.

Authors:  Alexander H Peden; Deep P Sarode; Carl R Mulholland; Marcelo A Barria; Diane L Ritchie; James W Ironside; Mark W Head
Journal:  Acta Neuropathol Commun       Date:  2014-10-21       Impact factor: 7.801
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