Literature DB >> 20977495

X-linked agammaglobulinemia complicated with endobronchial tuberculosis.

Chihiro Kawakami1, Akiko Inoue, Kimitaka Takitani, Hirokazu Kanegane, Toshio Miyawaki, Hiroshi Tamai.   

Abstract

AIM: We report a case of X-linked agammaglobulinemia complicated with endobronchial tuberculosis.
METHODS: We observed the patient's clinical course and analysed his data retrospectively.
RESULTS: Interestingly, the T-cell proliferation activity in this patient was intact, and the CD4-positive T cells produced interferon gamma. However, the result of the quantiferon alpha-2b test was negative.
CONCLUSION: The findings of this case suggest that the quantiferon alpha-2b test may not be diagnostic for tuberculosis not only in patients with T-cell disorders but also in cases with B-cell deficiencies such as X-linked agammaglobulinemia.
© 2010 The Author(s)/Acta Paediatrica © 2010 Foundation Acta Paediatrica.

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Year:  2010        PMID: 20977495     DOI: 10.1111/j.1651-2227.2010.02071.x

Source DB:  PubMed          Journal:  Acta Paediatr        ISSN: 0803-5253            Impact factor:   2.299


  4 in total

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4.  Unbalanced serum immunoglobulins in clinical subtypes of pediatric tuberculosis disease.

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  4 in total

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