Literature DB >> 20821215

Detection of RASA1 mutations in patients with sporadic Sturge-Weber syndrome.

Qin Zhou1, Jia-wei Zheng, Xiu-juan Yang, Hui-jun Wang, Duan Ma, Zhong-ping Qin.   

Abstract

OBJECTIVE: The aim of this study was to identify RASA1 mutation in Chinese population with sporadic Sturge-Weber syndrome (SWS).
METHODS: Genomic DNA was obtained from peripheral blood of nine patients with sporadic SWS. The 25 exons, promoter regions (-1,000 bp) as well as intron-exon boundaries of RASA1 were amplified by polymerase chain reaction, and products were sequenced directly.
RESULTS: A novel synonymous mutation (c.1229 G > A [p.K420K]) of RASA1 was identified in the present series.
CONCLUSION: It implied that RASA1 may be not a virulence gene, but further study is needed to know RASA1 gene mutation in SWS patients.

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Year:  2010        PMID: 20821215     DOI: 10.1007/s00381-010-1258-z

Source DB:  PubMed          Journal:  Childs Nerv Syst        ISSN: 0256-7040            Impact factor:   1.475


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