Warning: Undefined array key "mm" in /www/wwwroot/www.ai-bt.com/si.php on line 10 Deprecated: trim(): Passing null to parameter #1 ($string) of type string is deprecated in /www/wwwroot/www.ai-bt.com/si.php on line 10 Leukocyte adhesion deficiency type 1 presenting with recurrent pyoderma gangrenosum and flaccid scarring.

Literature DB >> 20807363

Leukocyte adhesion deficiency type 1 presenting with recurrent pyoderma gangrenosum and flaccid scarring.

Claas H Hinze¹, Anne W Lucky, Kevin E Bove, Rebecca A Marsh, Jack H Bleesing, Murray H Passo.

Abstract

We report an 11-year-old boy with a longstanding history of recurrent pyoderma gangrenosum and abnormal wound healing who eventually developed a fatal invasive fungal infection. This article emphasizes the importance to consider leukocyte adhesion deficiency type 1 in the differential diagnosis of patients with recurrent skin ulcers.

Entities: Disease Species

Mesh：

Year: 2010 PMID： 20807363 DOI： 10.1111/j.1525-1470.2010.01260.x

Source DB: PubMed Journal: Pediatr Dermatol ISSN： 0736-8046 Impact factor: 1.588

Keyword Cloud
Cited

11 in total

Review 1. Hematologically important mutations: leukocyte adhesion deficiency (first update).

Authors: Edith van de Vijver; Anne Maddalena; Özden Sanal; Steven M Holland; Gulbu Uzel; Manisha Madkaikar; Martin de Boer; Karin van Leeuwen; M Yavuz Köker; Nima Parvaneh; Alain Fischer; S K Alex Law; Nigel Klein; F Ilhan Tezcan; Ekrem Unal; Turkan Patiroglu; Bernd H Belohradsky; Klaus Schwartz; Raz Somech; Taco W Kuijpers; Dirk Roos
Journal: Blood Cells Mol Dis Date: 2011-11-30 Impact factor: 3.039

2. Leukocyte adhesion deficiency-I with a novel intronic mutation presenting with pyoderma gangrenosum- like lesions.

Authors: Manisha Madkaikar; Khushnooma Italia; Maya Gupta; Mukesh Desai; Amita Aggarwal; Surjit Singh; Deepti Suri; Anju Mishra; Sushant Chavan; Kanjaksha Ghosh; Rishu Sarangal; Sunil Dogra
Journal: J Clin Immunol Date: 2015-04-16 Impact factor: 8.317

Leukocyte adhesion deficiency type 1 presenting with recurrent pyoderma gangrenosum and flaccid scarring.

Review 1. Hematologically important mutations: leukocyte adhesion deficiency (first update).

2. Leukocyte adhesion deficiency-I with a novel intronic mutation presenting with pyoderma gangrenosum- like lesions.

3. Leucocyte adhesion deficiency type 1 with developmental delay secondary to CMV infection and filiation questions.

4. Regulation of innate immune response to Candida albicans infections by αMβ2-Pra1p interaction.

5. Extensive phlegmon and pyoderma gangrenosum: diagnostic difficulties.

6. Pyoderma Gangrenosum-like Wounds in Leukocyte Adhesion Deficiency: Case Report and Review of Literature.

7. Leukocyte adhesion defect type 1 presenting with recurrent pyoderma gangrenosum.

Review 8. Skin manifestations of primary immune deficiency.

9. Pyoderma gangrenosum in a patient with common variable primary immunodeficiency.

10. Pyoderma gangrenosum in a patient with chronic granulomatous disease: A case report.