Literature DB >> 20711615

Anesthesia for a 16-month-old patient with Prader-Willi syndrome.

Basak C Meco1, Zekeriyya Alanoglu, Ozgur Sinan Cengiz, Neslihan Alkis.   

Abstract

Prader-Willi syndrome (PWS) is a rare disorder of chromosome abnormalities in which the paternal genes in chromosome 15 are lacking. The clinical course is characterized by hypotonia, hyperphagia, and morbid obesity. Both general and regional anesthesia in these patients is difficult due to morbid obesity and hypotonia. We report our anesthetic management in a patient with PWS with a body mass index (BMI) of 29.43 kg/m² who underwent orchiopexy and hypospadias repair. The clinical course of the patient was uneventful during the procedure and postoperative period. However, arrangements with a pediatric intensive care setting for the postoperative period are recommended for patients with PWS undergoing surgery.

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Year:  2010        PMID: 20711615     DOI: 10.1007/s00540-010-1005-3

Source DB:  PubMed          Journal:  J Anesth        ISSN: 0913-8668            Impact factor:   2.078


  8 in total

1.  Regional cerebral glucose metabolic abnormality in Prader-Willi syndrome: A 18F-FDG PET study under sedation.

Authors:  Sang Eun Kim; Dong-Kyu Jin; Sang Soo Cho; Ji-Hae Kim; Sungdo David Hong; Kyung Hoon Paik; Yoo Joung Oh; An Hee Kim; Eun Kyung Kwon; Yon Ho Choe
Journal:  J Nucl Med       Date:  2006-07       Impact factor: 10.057

2.  Cardiac abnormalities during anesthesia in a child with Prader-Willi syndrome.

Authors:  R A Milliken; D M Weintraub
Journal:  Anesthesiology       Date:  1975-11       Impact factor: 7.892

3.  Anaesthesia and Prader-Willi syndrome.

Authors:  O R Dearlove; A Dobson; M Super
Journal:  Paediatr Anaesth       Date:  1998       Impact factor: 2.556

4.  Anaesthetic considerations in the Prader-Willi syndrome.

Authors:  J F Mayhew; B Taylor
Journal:  Can Anaesth Soc J       Date:  1983-09

5.  Recommendations for the diagnosis and management of Prader-Willi syndrome.

Authors:  A P Goldstone; A J Holland; B P Hauffa; A C Hokken-Koelega; M Tauber
Journal:  J Clin Endocrinol Metab       Date:  2008-08-12       Impact factor: 5.958

6.  Monopharmacologic general anaesthesia with sevoflurane in paediatric patient with Prader-Willi syndrome.

Authors:  S Rinaldi; L Rizzo; A Di Filippo; S Secchi; G Paternoster; M S La Torre; C Pascente; M R Stanzani
Journal:  Minerva Anestesiol       Date:  2002-10       Impact factor: 3.051

7.  Anesthesia for pediatric patients with Prader-Willi syndrome: report of two cases.

Authors:  Chi-Hao Tseng; Chit Chen; Chung-Hang Wong; Shu-Yam Wong; Kit-Man Wong
Journal:  Chang Gung Med J       Date:  2003-06

8.  Anaesthesia and the Prader-Willi syndrome.

Authors:  J W Mackenzie
Journal:  J R Soc Med       Date:  1991-04       Impact factor: 18.000

  8 in total
  2 in total

1.  Anesthetic management of Prader-Willi syndrome: what if neuromuscular relaxants could not be avoided?

Authors:  Amit Jain; Indu Bala; Jeetinder Kaur Makkar
Journal:  J Anesth       Date:  2011-12-25       Impact factor: 2.078

2.  Anesthetic management with a neuromuscular relaxant and sugammadex in a patient with Prader-Willi syndrome: A case report.

Authors:  Kyung Woo Kim; Seung Hwan Kim; Eun Jin Ahn; Hyo Jin Kim; Hey Ran Choi; Si Ra Bang
Journal:  SAGE Open Med Case Rep       Date:  2020-06-03
  2 in total

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