Bilateral ocular involvement as a presentation of Waldenström's macroglobulinemia.

We describe a 54 years old female with Waldenstrom's macroglobulinemia who presented with a bilateral ocular involvement. Ophthalmic involvement in Waldenstrom's macroglobulinemia is very rare. In addition, to our knowledge, there are only a few reports in the literature in which a primary diagnosis was made on the basis of ocular involvement. Diagnosis of malignancy in our case was established on the basis of the presence of small lymphocytes in fine-needle aspiration cytology from the orbital mass and typical bone marrow aspiration immunophenotype for Waldenstrom's macroglobulinemia.