Literature DB >> 20682599

Polymorphisms and mutations in vWF and ADAMTS13 genes and their correlation with plasma levels of FVIII and vWF in patients with deep venous thrombosis.

Luis Fernando Bittar1, Erich Vinícius de Paula, Tayana B T Mello, Lúcia H Siqueira, Fernanda L A Orsi, Joyce M Annichino-Bizzacchi.   

Abstract

BACKGROUND: Increased levels of factor VIII (FVIII) are a prevalent and independent risk factor for deep venous thrombosis (DVT) and are affected by von Willebrand factor (vWF) levels. DESIGN AND METHODS: ADAMTS13 contributes to vWF levels, and we investigated genetic polymorphisms previously described to be associated with decreased levels of these proteins in 435 patients with DVT (126 M and 309 F; median age 37 years, range 18-68 years) and 580 controls (163 M and 417 F; median age 35 years, range 18-68 years). Subsequently, we investigated the relationship between the genotypes and plasma levels of FVIII, vWF, and DVT risk.
RESULTS: Patients with DVT showed higher plasma levels of FVIII:C, FVIII:Ag, and vWF:Ag (P < .001) when compared to controls. Patients and controls heterozygous for the 4751A>G polymorphism in the vWF gene presented decreased levels of vWF:Ag, FVIII:Ag, and FVIII:C (P < .001), but this was not a protective factor for DVT. Individuals heterozygous for 1852C>G polymorphism in ADAMTS13 gene, which is associated with reduced levels of ADAMTS13, had significantly elevated levels of vWF:Ag (P = .001), FVIII:Ag (P = .01), and FVIII:C (P = .02). However, this polymorphism was not a risk factor for DVT in our study. Heterozygosis for a new polymorphism identified in ADAMTS13 gene, 1787-26G>A, was significantly associated with elevated levels of FVIII:C (P = .02) when compared to wild type.
CONCLUSIONS: Despite the tempting assumption that genetic factors that change ADAMTS13 activity might modulate the risk of DVT by altering vWF and FVIII levels, the polymorphisms analyzed in this study did not correlate with DVT risk among patients investigated.

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Year:  2010        PMID: 20682599     DOI: 10.1177/1076029610375815

Source DB:  PubMed          Journal:  Clin Appl Thromb Hemost        ISSN: 1076-0296            Impact factor:   2.389


  5 in total

1.  Von Willebrand factor is reversibly decreased during torpor in 13-lined ground squirrels.

Authors:  Scott Cooper; Shawn Sell; Luke Nelson; Jennifer Hawes; Jacob A Benrud; Bridget M Kohlnhofer; Bradley R Burmeister; Veronica H Flood
Journal:  J Comp Physiol B       Date:  2016-01       Impact factor: 2.200

2.  Role of factor VIII-binding capacity of endogenous von Willebrand factor in the development of factor VIII inhibitors in patients with severe hemophilia A.

Authors:  Yohann Repessé; Catherine Costa; Roberta Palla; Elika Farrokhi Moshai; Annie Borel-Derlon; Roseline D'Oiron; Chantal Rothschild; Amal El-Beshlawy; Mohsen Elalfy; Vijay Ramanan; Peyman Eshghi; Johannes Oldenburg; Anna Pavlova; Frits R Rosendaal; Flora Peyvandi; Srinivas V Kaveri; Sébastien Lacroix-Desmazes
Journal:  Haematologica       Date:  2019-01-31       Impact factor: 9.941

3.  Next-Generation Sequencing and In Vitro Expression Study of ADAMTS13 Single Nucleotide Variants in Deep Vein Thrombosis.

Authors:  Maria Teresa Pagliari; Luca A Lotta; Hugoline G de Haan; Carla Valsecchi; Gloria Casoli; Silvia Pontiggia; Ida Martinelli; Serena M Passamonti; Frits R Rosendaal; Flora Peyvandi
Journal:  PLoS One       Date:  2016-11-01       Impact factor: 3.240

4.  The role of ADAMTS-13 and von Willebrand factor in cancer patients: Results from the Vienna Cancer and Thrombosis Study.

Authors:  Hanna L Obermeier; Julia Riedl; Cihan Ay; Silvia Koder; Peter Quehenberger; Rupert Bartsch; Alexandra Kaider; Christoph C Zielinski; Ingrid Pabinger
Journal:  Res Pract Thromb Haemost       Date:  2019-05-06

Review 5.  Pathogenesis of Two Faces of DVT: New Identity of Venous Thromboembolism as Combined Micro-Macrothrombosis via Unifying Mechanism Based on "Two-Path Unifying Theory" of Hemostasis and "Two-Activation Theory of the Endothelium".

Authors:  Jae C Chang
Journal:  Life (Basel)       Date:  2022-01-31
  5 in total

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