Consecutive spontaneous rupture of the lower pole renal artery and main renal artery due to type 1 neurofibromatosis.

We report on a 37-year-old man suffering from type 1 neurofibromatosis with spontaneous rupture of a lower pole artery of the right kidney. Two renal arteries with aneurysmal alterations were identified at angiography. We did not coil the lower pole artery because active bleeding had stopped. Eleven days later, the patient suffered a further spontaneous rupture to the right main renal artery, and nephrectomy was unavoidable. His recovery was rapid and unremarkable.