| Literature DB >> 2053800 |
Abstract
An 11 year old boy presented with severe acute hereditary coproporphyria. Despite supportive measures his condition deteriorated after admission. Haem arginate, started two days after presentation, produced appreciable inhibition of porphyrin precursor overproduction and clinical improvement.Entities:
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Year: 1991 PMID: 2053800 PMCID: PMC1793153 DOI: 10.1136/adc.66.6.730
Source DB: PubMed Journal: Arch Dis Child ISSN: 0003-9888 Impact factor: 3.791