| Literature DB >> 20492031 |
Matthew L Williams1, Stephanie Burns Wechsler, G Chad Hughes.
Abstract
Loeys-Dietz syndrome (LDS) is a recently described connective tissue disorder characterized by generalized arterial tortuosity and aggressive aortopathy that untreated leads to early death even at aortic dimensions as small as 4 cm. We report the case of a young man with LDS successfully treated for aortic root, arch, and thoracoabdominal pathology.Entities:
Mesh：
Year: 2010 PMID： 20492031 DOI： 10.1111/j.1540-8191.2009.00956.x
Source DB: PubMed Journal: J Card Surg ISSN： 0886-0440 Impact factor: 1.620