Literature DB >> 20490478

Delayed enhancement cardiac magnetic resonance imaging in propionic acidemia.

Satoru Iwashima1, Takamichi Ishikawa, Takehiko Ohzeki, Yusaku Endou.   

Abstract

We report on cardiomyopathy in propionic acidemia (PA) diagnosed using delayed-enhancement cardiac magnetic imaging (DECM) in a 27-year-old woman. DECM demonstrated hyperenhancement at the lateral wall of the left ventricle, suggesting myocardial changes occurring after a metabolic crisis, which improved during the convalescent period. DECM was useful for the diagnosis of cardiomyopathy in PA.

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Year:  2010        PMID： 20490478     DOI： 10.1007/s00246-010-9723-8

Source DB:  PubMed          Journal:  Pediatr Cardiol        ISSN： 0172-0643            Impact factor:   1.655


  10 in total

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Review 4.  Delayed enhancement cardiovascular magnetic resonance assessment of non-ischaemic cardiomyopathies.

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8.  Propionyl-L-carnitine-mediated improvement in contractile function of rat hearts oxidizing acetoacetate.

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  10 in total
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  2 in total

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