[Sudden growth of previously indolent scalp nodule].

Cylindromas are benign adnexal tumors with eccrine and apocrine differentiation. They may appear in combination with spiradenomas and trichoepitheliomas in patients with the Brooke-Spiegler syndrome. Malignant changes are rare; possible clues are ulceration, bleeding or sudden growth of the lesions. Cylindromas are often removed for cosmetic reasons. We present a case of scalp cylindromatosis in which a primary cutaneous adenoid-cystic carcinoma developed. The patient was treated with local surgical excision. As our case shows, histological evaluation is mandatory, even when the clinical diagnosis seems obvious.