Endoarterial scoring--a novel treatment for resistant pulmonary arterial lesions associated with Williams-Beuren syndrome.

A 7-year-old girl with Williams-Beuren syndrome had undergone multiple percutaneous interventions for resistant peripheral pulmonary arterial stenoses with primarily conventional high-pressure balloon dilatation, but also with use of a cutting balloon. On this occasion, we used the AngioSculpt (AngioScore, Alameda, California) to remodel her distal vessels bilaterally with good effect. We believe this to be the first report of its use in the pulmonary arterial circulation of man.