Literature DB >> 20225048

A case of adult periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis (PFAPA) syndrome associated with endocapillary proliferative glomerulonephritis.

Massimiliano Cazzato1, Rossella Neri, Niccolo Possemato, Rodolfo Puccini, Stefano Bombardieri.   

Abstract

PFAPA is an acronym for periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis. This syndrome has been usually described in pediatric patients and it generally resolves spontaneously. The endocapillary proliferative glomerulonephritis (EPG) is a glomerular injury characterized by hypercellularity in glomerular lumen and is caused by post-infectious or autoimmune diseases. In this paper, we describe the case of a 35-year-old man affected by PFAPA and EPG. To our knowledge this association has never been reported in the literature before.

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Year:  2010        PMID: 20225048     DOI: 10.1007/s10067-010-1420-8

Source DB:  PubMed          Journal:  Clin Rheumatol        ISSN: 0770-3198            Impact factor:   2.980


  8 in total

Review 1.  Lights and shadows in autoinflammatory syndromes from the childhood and adulthood perspective.

Authors:  Donato Rigante; Antonio Vitale; Marco Francesco Natale; Luca Cantarini
Journal:  Clin Rheumatol       Date:  2015-12-03       Impact factor: 2.980

Review 2.  The labyrinth of autoinflammatory disorders: a snapshot on the activity of a third-level center in Italy.

Authors:  Luca Cantarini; Antonio Vitale; Orso Maria Lucherini; Caterina De Clemente; Francesco Caso; Luisa Costa; Giacomo Emmi; Elena Silvestri; Flora Magnotti; Maria Cristina Maggio; Eugenia Prinzi; Giuseppe Lopalco; Bruno Frediani; Rolando Cimaz; Mauro Galeazzi; Donato Rigante
Journal:  Clin Rheumatol       Date:  2014-06-24       Impact factor: 2.980

Review 3.  Basic Characteristics of Adults with Periodic Fever, Aphthous Stomatitis, Pharyngitis, and Adenopathy Syndrome in Comparison with the Typical Pediatric Expression of Disease.

Authors:  Marco Cattalini; Martina Soliani; Donato Rigante; Giuseppe Lopalco; Florenzo Iannone; Mauro Galeazzi; Luca Cantarini
Journal:  Mediators Inflamm       Date:  2015-08-18       Impact factor: 4.711

4.  Analysis of the genetic basis of periodic fever with aphthous stomatitis, pharyngitis, and cervical adenitis (PFAPA) syndrome.

Authors:  Silvio Alessandro Di Gioia; Nicola Bedoni; Annette von Scheven-Gête; Federica Vanoni; Andrea Superti-Furga; Michaël Hofer; Carlo Rivolta
Journal:  Sci Rep       Date:  2015-05-19       Impact factor: 4.379

5.  Periodic fever, aphthous stomatitis, pharyngitis and cervical adenitis syndrome persisting to adulthood - an example of a diagnostic and therapeutic challenge.

Authors:  Ewa Więsik-Szewczyk; Beata Wolska-Kuśnierz; Karina Jahnz-Różyk
Journal:  Reumatologia       Date:  2019-10-31

Review 6.  New insights on multigenic autoinflammatory diseases.

Authors:  Petros Efthimiou; Olga Petryna; Priscila Nakasato; Apostolos Kontzias
Journal:  Ther Adv Musculoskelet Dis       Date:  2022-09-03       Impact factor: 3.625

7.  Caution Should be Used in the Recognition of Adult-Onset Autoinflammatory Disorders: Facts or Fiction?

Authors:  Luca Cantarini; Orso Maria Lucherini; Donato Rigante
Journal:  Front Immunol       Date:  2013-04-23       Impact factor: 7.561

8.  Diagnostic Criteria for Adult-Onset Periodic Fever, Aphthous Stomatitis, Pharyngitis, and Cervical Adenitis (PFAPA) Syndrome.

Authors:  Luca Cantarini; Antonio Vitale; Ludovico Luca Sicignano; Giacomo Emmi; Elena Verrecchia; Isabella Patisso; Lucia Cerrito; Claudia Fabiani; Gabriele Cevenini; Bruno Frediani; Mauro Galeazzi; Donato Rigante; Raffaele Manna
Journal:  Front Immunol       Date:  2017-08-24       Impact factor: 7.561

  8 in total

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