Literature DB >> 2015129

Lymphatic abnormalities in Alagille's syndrome.

D P Dutka1, C Cousins, A R Manhire.   

Abstract

Chylous pleural effusions developed in a patient with Alagille's syndrome who had dysplasia of the lymphatic system. Lymphatic abnormalities are not a recognised feature of Alagille's syndrome.

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Mesh：

Year:  1991        PMID： 2015129      PMCID： PMC1024546          DOI： 10.1136/hrt.65.3.168

Source DB:  PubMed          Journal:  Br Heart J        ISSN： 0007-0769


  6 in total

1.  Arteriohepatic dysplasia: familial pulmonary arterial stenosis with neonatal liver disease.

Authors:  G H Watson; V Miller
Journal:  Arch Dis Child       Date:  1973-06       Impact factor: 3.791

2.  Congenital heart disease in patients with primary lymphedemas.

Authors:  C R Corbett; R F Dale; D J Coltart; J B Kinmonth
Journal:  Lymphology       Date:  1982-09       Impact factor: 1.286

3.  Arteriohepatic dysplasia: a benign syndrome of intrahepatic cholestasis with multiple organ involvement.

Authors:  C A Riely; E Cotlier; P S Jensen; G Klatskin
Journal:  Ann Intern Med       Date:  1979-10       Impact factor: 25.391

4.  Hepatic ductular hypoplasia associated with characteristic facies, vertebral malformations, retarded physical, mental, and sexual development, and cardiac murmur.

Authors:  D Alagille; M Odièvre; M Gautier; J P Dommergues
Journal:  J Pediatr       Date:  1975-01       Impact factor: 4.406

5.  A father and son with cholestasis and peripheral pulmonic stenosis: a distinct form of intrahepatic cholestasis.

Authors:  C A Riely; D R LaBrecque; C Ghent; A Horwich; G Klatskin
Journal:  J Pediatr       Date:  1978-03       Impact factor: 4.406

6.  Arteriohepatic dysplasia: radiologic features of a new syndrome.

Authors:  N S Rosenfield; M J Kelley; P S Jensen; E Cotlier; A T Rosenfield; C A Riely
Journal:  AJR Am J Roentgenol       Date:  1980-12       Impact factor: 3.959
  6 in total
  4 in total

1.  Altered lymphatics in an ovine model of congenital heart disease with increased pulmonary blood flow.

Authors:  Sanjeev A Datar; Eric G Johnson; Peter E Oishi; Michael Johengen; Eric Tang; Angela Aramburo; Jubilee Barton; Hsuan-Chang Kuo; Stephen Bennett; Konstantine Xoinis; Bhupinder Reel; Gokhan Kalkan; Eniko Sajti; Oscar Osorio; Gary W Raff; Michael A Matthay; Jeffrey R Fineman
Journal:  Am J Physiol Lung Cell Mol Physiol       Date:  2011-12-29       Impact factor: 5.464

2.  Altered reactivity and nitric oxide signaling in the isolated thoracic duct from an ovine model of congenital heart disease with increased pulmonary blood flow.

Authors:  Sanjeev A Datar; Peter E Oishi; Wenhui Gong; Stephen H Bennett; Christine E Sun; Michael Johengen; Jun Maki; Rebecca C Johnson; Gary W Raff; Jeffrey R Fineman
Journal:  Am J Physiol Heart Circ Physiol       Date:  2014-02-14       Impact factor: 4.733

3.  Disrupted NOS signaling in lymphatic endothelial cells exposed to chronically increased pulmonary lymph flow.

Authors:  Sanjeev A Datar; Wenhui Gong; Youping He; Michael Johengen; Rebecca J Kameny; Gary W Raff; Emin Maltepe; Peter E Oishi; Jeffrey R Fineman
Journal:  Am J Physiol Heart Circ Physiol       Date:  2016-05-13       Impact factor: 4.733

4.  Expanded phenotypic spectrum of JAG1-associated diseases: Central conducting lymphatic anomaly with a pathogenic variant in JAG1.

Authors:  Dong Li; Sarah E Sheppard; Christina Peroutka; Caitlin Barnes; Janet R Reid; Christopher L Smith; Yoav Dori; Hakon Hakonarson
Journal:  Clin Genet       Date:  2021-01-12       Impact factor: 4.438
  4 in total

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