Literature DB >> 20075170

aHUS: a disorder with many risk factors.

Santiago Rodríguez de Córdoba1.   

Abstract

Year:  2010        PMID: 20075170     DOI: 10.1182/blood-2009-11-252627

Source DB:  PubMed          Journal:  Blood        ISSN: 0006-4971            Impact factor:   22.113


× No keyword cloud information.
  12 in total

1.  Atypical haemolytic-uraemic syndrome due to heterozygous mutations of CFH/CFHR1-3 and complement factor H 479.

Authors:  Preeti Chaudhary; Mehmet Hepgur; Sarmen Sarkissian; Richard J H Smith; Ilene C Weitz
Journal:  Blood Transfus       Date:  2013-11-15       Impact factor: 3.443

Review 2.  Autoimmunity: homeostasis of innate immunity gone awry.

Authors:  Hyon Ju Park; John P Atkinson
Journal:  J Clin Immunol       Date:  2012-10-11       Impact factor: 8.317

3.  Factor I autoantibodies in patients with atypical hemolytic uremic syndrome: disease-associated or an epiphenomenon?

Authors:  David Kavanagh; Isabel Y Pappworth; Holly Anderson; Christine M Hayes; Iain Moore; Eva-Maria Hunze; Karim Bennaceur; Pietro Roversi; Susan Lea; Lisa Strain; Roy Ward; Nick Plant; Corina Nailescu; Timothy H J Goodship; Kevin J Marchbank
Journal:  Clin J Am Soc Nephrol       Date:  2012-01-05       Impact factor: 8.237

4.  Complement factor H-related protein 1 deficiency and factor H antibodies in pediatric patients with atypical hemolytic uremic syndrome.

Authors:  Johannes Hofer; Andreas R Janecke; L B Zimmerhackl; Magdalena Riedl; Alejandra Rosales; Thomas Giner; Gerard Cortina; Carola J Haindl; Barbara Petzelberger; Miriam Pawlik; Verena Jeller; Udo Vester; Bettina Gadner; Michael van Husen; Michael L Moritz; Reinhard Würzner; Therese Jungraithmayr
Journal:  Clin J Am Soc Nephrol       Date:  2012-12-14       Impact factor: 8.237

Review 5.  Genetics and complement in atypical HUS.

Authors:  David Kavanagh; Tim Goodship
Journal:  Pediatr Nephrol       Date:  2010-06-06       Impact factor: 3.714

Review 6.  Defective complement inhibitory function predisposes to renal disease.

Authors:  Anuja Java; John Atkinson; Jane Salmon
Journal:  Annu Rev Med       Date:  2012-11-01       Impact factor: 13.739

7.  Complement activity and complement regulatory gene mutations are associated with thrombosis in APS and CAPS.

Authors:  Shruti Chaturvedi; Evan M Braunstein; Xuan Yuan; Jia Yu; Alice Alexander; Hang Chen; Eleni Gavriilaki; Ravi Alluri; Michael B Streiff; Michelle Petri; Mark A Crowther; Keith R McCrae; Robert A Brodsky
Journal:  Blood       Date:  2020-01-23       Impact factor: 25.476

8.  Adjustment of Eculizumab Dosage Pattern in Patients with Atypical Hemolytic Uremic Syndrome with Suboptimal Response to Standard Treatment Pattern.

Authors:  Camino García Monteavaro; Carmen Peralta Roselló; Borja Quiroga; José María Baltar Martín; Lorena Castillo Eraso; Fernando de Álvaro Moreno; Alberto Martínez Vea; María Teresa Visus-Fernández de Manzanos
Journal:  Case Rep Nephrol       Date:  2016-11-29

Review 9.  Familial atypical hemolytic uremic syndrome: a review of its genetic and clinical aspects.

Authors:  Fengxiao Bu; Nicolo Borsa; Ardissino Gianluigi; Richard J H Smith
Journal:  Clin Dev Immunol       Date:  2012-11-08

10.  Risk of Atypical HUS Among Family Members of Patients Carrying Complement Regulatory Gene Abnormality.

Authors:  Gianluigi Ardissino; Selena Longhi; Luigi Porcaro; Giulia Pintarelli; Bice Strumbo; Valentina Capone; Donata Cresseri; Giulia Loffredo; Francesca Tel; Stefania Salardi; Martina Sgarbanti; Laura Martelli; Evangeline Millicent Rodrigues; Nicolò Borsa-Ghiringhelli; Giovanni Montini; Manuela Seia; Massimo Cugno; Fabio Carfagna; Dario Consonni; Silvana Tedeschi
Journal:  Kidney Int Rep       Date:  2021-03-25
View more

北京卡尤迪生物科技股份有限公司 © 2022-2023.