| Literature DB >> 19943169 |
G D Maurer, J Schittenhelm, U Ernemann, V A J Kempf, R Ritz, M Weller, F Schmidt.
Abstract
POEMS syndrome is a rare multi-system disease with typical features of polyneuropathy, organomegaly, endocrinopathy, monoclonal plasmaproliferative disorder and skin changes. We describe a 44-year-old woman with polyneuropathy, hepatomegaly, IgA lambda-plasmacytoma, thrombocytosis, papilledema with elevated protein levels in cerebrospinal fluid and multiple cutaneous hemangiomas who was diagnosed with three intracranial lesions. Histology revealed capillary hemangiomas, one of them displaying partially glomeruloid features.Entities:
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Year: 2009 PMID： 19943169 DOI： 10.1007/s00415-009-5398-6
Source DB: PubMed Journal: J Neurol ISSN： 0340-5354 Impact factor: 4.849