Literature DB >> 19921367

Congenital erythropoietic porphyria: anesthetic implications.

Mritunjay Kumar1, Somnath Bose, Vanlal Darlong, Jyotsna Punj.   

Abstract

Congenital erythropoietic porphyria is a rare error of heme metabolism. Derangement of heme metabolism leads to disfiguration, phototoxicity, and the precipitation of porphyric crises. This case report discusses the myriad perioperative considerations in a patient with congenital erythropoietic porphyria.

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Year:  2009        PMID: 19921367     DOI: 10.1007/s00540-009-0784-x

Source DB:  PubMed          Journal:  J Anesth        ISSN: 0913-8668            Impact factor:   2.078


  6 in total

Review 1.  Porphyrias.

Authors:  M F James; R J Hift
Journal:  Br J Anaesth       Date:  2000-07       Impact factor: 9.166

Review 2.  Congenital erythropoietic porphyria: advances in pathogenesis and treatment.

Authors:  Robert J Desnick; Kenneth H Astrin
Journal:  Br J Haematol       Date:  2002-06       Impact factor: 6.998

3.  Anesthetic management for congenital erythropoietic porphyria: report of a case.

Authors:  A Nakamura; M Wakamatsu; H Tsunobuchi
Journal:  J Anesth       Date:  1999       Impact factor: 2.078

4.  Perioperative measures during liver transplantation for erythropoietic protoporphyria.

Authors:  L Meerman; R Verwer; M J Slooff; J van Hattum; G J Beukeveld; J H Kleibeuker; E B Haagsma
Journal:  Transplantation       Date:  1994-01       Impact factor: 4.939

Review 5.  Anesthetic considerations in porphyrias.

Authors:  N F Jensen; D S Fiddler; V Striepe
Journal:  Anesth Analg       Date:  1995-03       Impact factor: 5.108

6.  Anaesthetic management of a patient with erythropoietic protoporphyria for ventricular septal defect closure.

Authors:  B Asokumar; C Kierney; T W James; J Amato; K J Tumanmd
Journal:  Paediatr Anaesth       Date:  1999       Impact factor: 2.556

  6 in total
  1 in total

1.  Sugammadex and amino acid infusion can contribute to safe anesthetic management of variegate porphyria.

Authors:  Yoshitaka Aoki; Kazuyuki Atsumi; Makiko Kora; Naoko Koh; Junichiro Yokoyama
Journal:  JA Clin Rep       Date:  2018-06-18
  1 in total

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