Literature DB >> 19773169

Isolated inflammatory myopathy with rimmed vacuoles presenting with dropped head.

Hiroshi Kataoka1, Kazuma Sugie, Mari Terashima, Munehisa Koizumi, Hirosei Horikawa, Ichizo Nishino, Ikuya Nonaka, Satoshi Ueno.   

Abstract

We describe an unusual case of inflammatory myopathy with rimmed vacuoles associated with dropped head syndrome. Muscle biopsy in our patient revealed variations in fiber size with fiber necrosis and regeneration, accompanied by many rimmed vacuoles and areas of endomysial cell infiltration. Electron microscopy demonstrated autophagic vacuoles and tubulofilamentous inclusions. This myopathy can cause dropped head syndrome in a subgroup of patients.

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Year:  2009        PMID: 19773169     DOI: 10.1016/j.nmd.2009.08.006

Source DB:  PubMed          Journal:  Neuromuscul Disord        ISSN: 0960-8966            Impact factor:   4.296


  2 in total

1.  Anti-mitochondrial antibody-associated myositis with eosinophilia and dropped head.

Authors:  Hayato Shimizu; Ichizo Nishino; Tetsuhiro Ueda; Nobuo Kohara; Hiroaki Nishioka
Journal:  eNeurologicalSci       Date:  2018-05-23

2.  Dropped head syndrome: diagnosis and management.

Authors:  Allan R Martin; Rajesh Reddy; Michael G Fehlings
Journal:  Evid Based Spine Care J       Date:  2011-05
  2 in total

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