| Literature DB >> 19773169 |
Hiroshi Kataoka1, Kazuma Sugie, Mari Terashima, Munehisa Koizumi, Hirosei Horikawa, Ichizo Nishino, Ikuya Nonaka, Satoshi Ueno.
Abstract
We describe an unusual case of inflammatory myopathy with rimmed vacuoles associated with dropped head syndrome. Muscle biopsy in our patient revealed variations in fiber size with fiber necrosis and regeneration, accompanied by many rimmed vacuoles and areas of endomysial cell infiltration. Electron microscopy demonstrated autophagic vacuoles and tubulofilamentous inclusions. This myopathy can cause dropped head syndrome in a subgroup of patients.Entities:
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Year: 2009 PMID: 19773169 DOI: 10.1016/j.nmd.2009.08.006
Source DB: PubMed Journal: Neuromuscul Disord ISSN: 0960-8966 Impact factor: 4.296