Literature DB >> 19762313

Growth hormone therapy in neonatal patients with methylmalonic acidemia.

Chuan-Hong Kao1, Mei-Ying Liu, Tze-Tze Liu, Kwang-Jen Hsiao, Kang-Hsiang Cheng, Cheng-Hung Huang, Hsiang-Yu Lin, Dau-Ming Niu.   

Abstract

BACKGROUND: Information regarding growth hormone (GH) therapy in neonatal patients with methylmalonic academia (MMA) is lacking. We present our experience with GH therapy in neonatal patients with MMA.
METHODS: Four neonatal patients with mut 0 type MMA were identified through newborn screening for elevated propionylcarnitine (C3) levels. GH therapy (0.6 IU/kg/week, subcutaneously) was prescribed for patient 1 after 1 month of admission, and was prescribed for patients 2, 3 and 4 on the 1st day of admission. We evaluated weight, skin erosion, hospital stay, and serum levels of C3 after GH therapy.
RESULTS: All of the neonatal patients with MMA displayed obvious weight gain and distinct improvement in skin erosions after GH therapy. The duration of hospital stay for patients 2, 3 and 4 was reduced compared to that of patient 1. However, the metabolic effects of GH therapy on reducing serum levels of C3 seem to be indeterminate.
CONCLUSION: Our clinical findings suggest that GH therapy has potentially beneficial effects on neonatal patients with MMA.

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Year:  2009        PMID: 19762313     DOI: 10.1016/S1726-4901(09)70408-3

Source DB:  PubMed          Journal:  J Chin Med Assoc        ISSN: 1726-4901            Impact factor:   2.743


  6 in total

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6.  Pre-implantation genetic diagnosis in an Iranian family with a novel mutation in MUT gene.

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  6 in total

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