Literature DB >> 19741216

Mutations in FUS cause FALS and SALS in French and French Canadian populations.

V V Belzil1, P N Valdmanis, P A Dion, H Daoud, E Kabashi, A Noreau, J Gauthier, P Hince, A Desjarlais, J-P Bouchard, L Lacomblez, F Salachas, P-F Pradat, W Camu, V Meininger, N Dupré, G A Rouleau.   

Abstract

BACKGROUND: The identification of mutations in the TARDBP and more recently the identification of mutations in the FUS gene as the cause of amyotrophic lateral sclerosis (ALS) is providing the field with new insight about the mechanisms involved in this severe neurodegenerative disease.
METHODS: To extend these recent genetic reports, we screened the entire gene in a cohort of 200 patients with ALS. An additional 285 patients with sporadic ALS were screened for variants in exon 15 for which mutations were previously reported.
RESULTS: In total, 3 different mutations were identified in 4 different patients, including 1 3-bp deletion in exon 3 of a patient with sporadic ALS and 2 missense mutations in exon 15 of 1 patient with familial ALS and 2 patients with sporadic ALS.
CONCLUSIONS: Our study identified sporadic patients with mutations in the FUS gene. The accumulation and description of different genes and mutations helps to develop a more comprehensive picture of the genetic events underlying amyotrophic lateral sclerosis.

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Year:  2009        PMID: 19741216      PMCID: PMC3462471          DOI: 10.1212/WNL.0b013e3181bbfeef

Source DB:  PubMed          Journal:  Neurology        ISSN: 0028-3878            Impact factor:   9.910


  10 in total

1.  Fus deficiency in mice results in defective B-lymphocyte development and activation, high levels of chromosomal instability and perinatal death.

Authors:  G G Hicks; N Singh; A Nashabi; S Mai; G Bozek; L Klewes; D Arapovic; E K White; M J Koury; E M Oltz; L Van Kaer; H E Ruley
Journal:  Nat Genet       Date:  2000-02       Impact factor: 38.330

2.  Male sterility and enhanced radiation sensitivity in TLS(-/-) mice.

Authors:  M Kuroda; J Sok; L Webb; H Baechtold; F Urano; Y Yin; P Chung; D G de Rooij; A Akhmedov; T Ashley; D Ron
Journal:  EMBO J       Date:  2000-02-01       Impact factor: 11.598

3.  The RNA binding protein TLS is translocated to dendritic spines by mGluR5 activation and regulates spine morphology.

Authors:  Ritsuko Fujii; Shigeo Okabe; Tomoe Urushido; Kiyoshi Inoue; Atsushi Yoshimura; Taro Tachibana; Toru Nishikawa; Geoffrey G Hicks; Toru Takumi
Journal:  Curr Biol       Date:  2005-03-29       Impact factor: 10.834

4.  Ubiquitinated TDP-43 in frontotemporal lobar degeneration and amyotrophic lateral sclerosis.

Authors:  Manuela Neumann; Deepak M Sampathu; Linda K Kwong; Adam C Truax; Matthew C Micsenyi; Thomas T Chou; Jennifer Bruce; Theresa Schuck; Murray Grossman; Christopher M Clark; Leo F McCluskey; Bruce L Miller; Eliezer Masliah; Ian R Mackenzie; Howard Feldman; Wolfgang Feiden; Hans A Kretzschmar; John Q Trojanowski; Virginia M-Y Lee
Journal:  Science       Date:  2006-10-06       Impact factor: 47.728

5.  TLS facilitates transport of mRNA encoding an actin-stabilizing protein to dendritic spines.

Authors:  Ritsuko Fujii; Toru Takumi
Journal:  J Cell Sci       Date:  2005-11-29       Impact factor: 5.285

6.  Fusion of the dominant negative transcription regulator CHOP with a novel gene FUS by translocation t(12;16) in malignant liposarcoma.

Authors:  T H Rabbitts; A Forster; R Larson; P Nathan
Journal:  Nat Genet       Date:  1993-06       Impact factor: 38.330

Review 7.  ALS and FTLD: two faces of TDP-43 proteinopathy.

Authors:  R M Liscic; L T Grinberg; J Zidar; M A Gitcho; N J Cairns
Journal:  Eur J Neurol       Date:  2008-08       Impact factor: 6.089

8.  Mutations in Cu/Zn superoxide dismutase gene are associated with familial amyotrophic lateral sclerosis.

Authors:  D R Rosen; T Siddique; D Patterson; D A Figlewicz; P Sapp; A Hentati; D Donaldson; J Goto; J P O'Regan; H X Deng
Journal:  Nature       Date:  1993-03-04       Impact factor: 49.962

9.  Mutations in the FUS/TLS gene on chromosome 16 cause familial amyotrophic lateral sclerosis.

Authors:  T J Kwiatkowski; D A Bosco; A L Leclerc; E Tamrazian; C R Vanderburg; C Russ; A Davis; J Gilchrist; E J Kasarskis; T Munsat; P Valdmanis; G A Rouleau; B A Hosler; P Cortelli; P J de Jong; Y Yoshinaga; J L Haines; M A Pericak-Vance; J Yan; N Ticozzi; T Siddique; D McKenna-Yasek; P C Sapp; H R Horvitz; J E Landers; R H Brown
Journal:  Science       Date:  2009-02-27       Impact factor: 47.728

10.  Mutations in FUS, an RNA processing protein, cause familial amyotrophic lateral sclerosis type 6.

Authors:  Caroline Vance; Boris Rogelj; Tibor Hortobágyi; Kurt J De Vos; Agnes Lumi Nishimura; Jemeen Sreedharan; Xun Hu; Bradley Smith; Deborah Ruddy; Paul Wright; Jeban Ganesalingam; Kelly L Williams; Vineeta Tripathi; Safa Al-Saraj; Ammar Al-Chalabi; P Nigel Leigh; Ian P Blair; Garth Nicholson; Jackie de Belleroche; Jean-Marc Gallo; Christopher C Miller; Christopher E Shaw
Journal:  Science       Date:  2009-02-27       Impact factor: 47.728

  10 in total
  53 in total

Review 1.  The present and the future of neuroimaging in amyotrophic lateral sclerosis.

Authors:  F Agosta; A Chiò; M Cosottini; N De Stefano; A Falini; M Mascalchi; M A Rocca; V Silani; G Tedeschi; M Filippi
Journal:  AJNR Am J Neuroradiol       Date:  2010-04-01       Impact factor: 3.825

2.  De novo truncating FUS gene mutation as a cause of sporadic amyotrophic lateral sclerosis.

Authors:  Mariely DeJesus-Hernandez; Jannet Kocerha; NiCole Finch; Richard Crook; Matt Baker; Pamela Desaro; Amelia Johnston; Nicola Rutherford; Aleksandra Wojtas; Kathleen Kennelly; Zbigniew K Wszolek; Neill Graff-Radford; Kevin Boylan; Rosa Rademakers
Journal:  Hum Mutat       Date:  2010-05       Impact factor: 4.878

Review 3.  TAR DNA-binding protein 43 in neurodegenerative disease.

Authors:  Alice S Chen-Plotkin; Virginia M-Y Lee; John Q Trojanowski
Journal:  Nat Rev Neurol       Date:  2010-03-16       Impact factor: 42.937

Review 4.  RNA processing pathways in amyotrophic lateral sclerosis.

Authors:  Marka van Blitterswijk; John E Landers
Journal:  Neurogenetics       Date:  2010-03-27       Impact factor: 2.660

Review 5.  Clinical neurogenetics: amyotrophic lateral sclerosis.

Authors:  Matthew B Harms; Robert H Baloh
Journal:  Neurol Clin       Date:  2013-11       Impact factor: 3.806

6.  Nuclear localization sequence of FUS and induction of stress granules by ALS mutants.

Authors:  Jozsef Gal; Jiayu Zhang; David M Kwinter; Jianjun Zhai; Hongge Jia; Jianhang Jia; Haining Zhu
Journal:  Neurobiol Aging       Date:  2010-07-31       Impact factor: 4.673

Review 7.  The tip of the iceberg: RNA-binding proteins with prion-like domains in neurodegenerative disease.

Authors:  Oliver D King; Aaron D Gitler; James Shorter
Journal:  Brain Res       Date:  2012-01-21       Impact factor: 3.252

8.  A de novo missense mutation of the FUS gene in a "true" sporadic ALS case.

Authors:  Adriano Chiò; Andrea Calvo; Cristina Moglia; Irene Ossola; Maura Brunetti; Luca Sbaiz; Shiao-lin Lai; Yevgeniya Abramzon; Bryan J Traynor; Gabriella Restagno
Journal:  Neurobiol Aging       Date:  2010-07-03       Impact factor: 4.673

9.  De novo nonsense mutation of the FUS gene in an apparently familial amyotrophic lateral sclerosis case.

Authors:  Andrea Calvo; Cristina Moglia; Antonio Canosa; Maura Brunetti; Marco Barberis; Bryan J Traynor; Giovanna Carrara; Consuelo Valentini; Gabriella Restagno; Adriano Chiò
Journal:  Neurobiol Aging       Date:  2013-12-27       Impact factor: 4.673

10.  Proteomic analysis of FUS interacting proteins provides insights into FUS function and its role in ALS.

Authors:  Marisa Kamelgarn; Jing Chen; Lisha Kuang; Alexandra Arenas; Jianjun Zhai; Haining Zhu; Jozsef Gal
Journal:  Biochim Biophys Acta       Date:  2016-07-25
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