Triple lumbar dermal sinuses: unusual presentation of a typically solitary midline lesion.

BACKGROUND: Congenital dermal sinus is a type of closed spinal dysraphism caused by incomplete disjunction. The lesion occurs everywhere along neuraxis predominantly as a solitary midline sinus in the lumbosacral area. CASE HISTORY: The authors report on a 10-month-old girl with triple congenital dermal sinuses associated with dermoid tumors and intradural extension of one of them. DISCUSSION: Triple dermal sinuses of the lumbosacral area in a single patient have never been described previously. Incomplete disjunction is suggested to cause this abnormality thereafter the orifice may be divided to three sinuses and some mesenchymal tissues separated the two proximal sinuses to a paramedian location. 2009 S. Karger AG, Basel