Periureteric venous ring with renal calculi and transitional cell carcinoma: report of a rare case.

We describe a very rare congenital anomaly of the inferior vena cava in a case who presented with renal calculi and transitional cell carcinoma on the right side. The diagnosis of 'periureteric venous ring' was made on preoperative imaging and confirmed on surgical exploration. We also review the literature and discuss the embryological origin of this anomaly along with its clinical significance.