Literature DB >> 19567621

Congenital heart block not associated with anti-Ro/La antibodies: comparison with anti-Ro/La-positive cases.

Antonio Brucato1, Chiara Grava, Maria Bortolati, Keigo Ikeda, Ornella Milanesi, Rolando Cimaz, Veronique Ramoni, Gabriele Vignati, Stefano Martinelli, Youcef Sadou, Adele Borghi, Angela Tincani, Edward K L Chan, Amelia Ruffatti.   

Abstract

OBJECTIVE: To study anti-Ro/La-negative congenital heart block (CHB).
METHODS: Forty-five fetuses with CHB were evaluated by analysis of anti-Ro/La antibodies using sensitive laboratory methods.
RESULTS: There were 9 cases of anti-Ro/La-negative CHB; 3 died (33.3%). Only 3 (33.3%) were complete in utero and 5 (55.5%) were unstable. No specific etiology was diagnosed. Six infants (66.6%) were given pacemakers. There were 36 cases of anti-Ro/La-positive CHB. All except 2 infants (94.4%) had complete atrioventricular block in utero. Ten died (27.8%), one (2.7%) developed severe dilated cardiomyopathy, and 26 (72.2%) were given pacemakers.
CONCLUSION: Nine of the 45 consecutive CHB cases (20%) were anti-Ro/La-negative with no known cause. They were less stable and complete than the anti-Ro/La positive cases.

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Year:  2009        PMID: 19567621      PMCID: PMC2798588          DOI: 10.3899/jrheum.080737

Source DB:  PubMed          Journal:  J Rheumatol        ISSN: 0315-162X            Impact factor:   4.666


  15 in total

1.  Anti-SSA/Ro-related congenital heart block in two family members of different generations: Comment on the article by Clancy et al.

Authors:  Amelia Ruffatti; Maria Favaro; Franco Cozzi; Marta Tonello; Chiara Grava; Paolo Lazzarin; Ornella Milanesi; Piero Marson; Alessandra Balboni; Antonio Brucato
Journal:  Arthritis Rheum       Date:  2005-05

2.  Presentation and prognosis of complete atrioventricular block in childhood, according to maternal antibody status.

Authors:  Elisabeth Villain; Nathalie Coastedoat-Chalumeau; Eloi Marijon; Younes Boudjemline; Jean-Charles Piette; Damien Bonnet
Journal:  J Am Coll Cardiol       Date:  2006-09-26       Impact factor: 24.094

3.  Perinatal outcome of fetus with isolated congenital second degree atrioventricular block without maternal anti-SSA/Ro-SSB/La antibodies.

Authors:  Yao-Lung Chang; Peter C C Hsieh; Shuenn-Dyh Chang; An-Shine Chao; Ching Chung Liang; Yung-Kuei Soong
Journal:  Eur J Obstet Gynecol Reprod Biol       Date:  2005-10-01       Impact factor: 2.435

4.  Atrioventricular block detected in fetal life: associated anomalies and potential prognostic markers.

Authors:  C Berg; A Geipel; T Kohl; J Breuer; U Germer; M Krapp; A A Baschat; M Hansmann; U Gembruch
Journal:  Ultrasound Obstet Gynecol       Date:  2005-07       Impact factor: 7.299

5.  Perinatal outcome of fetal complete atrioventricular block: a multicenter experience.

Authors:  K G Schmidt; H E Ulmer; N H Silverman; C S Kleinman; J A Copel
Journal:  J Am Coll Cardiol       Date:  1991-05       Impact factor: 24.094

6.  Outcome of isolated congenital complete heart block diagnosed in utero.

Authors:  A M Groves; L D Allan; E Rosenthal
Journal:  Heart       Date:  1996-02       Impact factor: 5.994

7.  Clinical course of fetal congenital atrioventricular block in the Japanese population: a multicentre experience.

Authors:  Y Maeno; W Himeno; A Saito; S Hiraishi; O Hirose; M Ikuma; N Inamura; M Kawataki; A Mizukami; M Ota; H Shiraishi; G Satomi; H Kato
Journal:  Heart       Date:  2005-08       Impact factor: 5.994

8.  Transient non-autoimmune fetal heart block.

Authors:  Johannes M P J Breur; Martijn A Oudijk; Philip Stoutenbeek; Gerard H A Visser; Erik J Meijboom
Journal:  Fetal Diagn Ther       Date:  2005 Mar-Apr       Impact factor: 2.587

9.  Perinatal outcome of fetal atrioventricular block: one-hundred-sixteen cases from a single institution.

Authors:  Lilian M Lopes; Gláucia Maria Penha Tavares; Ana Paula Damiano; Marco Antônio Borges Lopes; Vera Demarchi Aiello; Regina Schultz; Marcelo Zugaib
Journal:  Circulation       Date:  2008-09-02       Impact factor: 29.690

Review 10.  Epidemiology, etiology, detection, and treatment of autoantibody-associated congenital heart block in neonatal lupus.

Authors:  Deborah M Friedman; Ann Rupel; Jill P Buyon
Journal:  Curr Rheumatol Rep       Date:  2007-05       Impact factor: 4.592

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  10 in total

1.  Doppler fetal mechanical PR interval prolongation with positive maternal anti-RNP but negative SSA/Ro and SSB/La auto-antibodies.

Authors:  Ruben J Acherman; Deborah M Friedman; Jill P Buyon; Joel Schwartz; William J Castillo; Robert C Rollins; William N Evans
Journal:  Prenat Diagn       Date:  2010-08       Impact factor: 3.050

2.  Isolated congenital heart block.

Authors:  F Sedef Tunaoglu; Ayse Yildirim; Dogus Vurali
Journal:  Tex Heart Inst J       Date:  2010

Review 3.  The clinical spectrum of autoimmune congenital heart block.

Authors:  Pilar Brito-Zerón; Peter M Izmirly; Manuel Ramos-Casals; Jill P Buyon; Munther A Khamashta
Journal:  Nat Rev Rheumatol       Date:  2015-03-24       Impact factor: 20.543

Review 4.  Pregnancy outcomes in patients with autoimmune diseases and anti-Ro/SSA antibodies.

Authors:  Antonio Brucato; Rolando Cimaz; Roberto Caporali; Véronique Ramoni; Jill Buyon
Journal:  Clin Rev Allergy Immunol       Date:  2011-02       Impact factor: 8.667

5.  Correlation of Maternal Autoantibodies with Fetal Congenital Heart Block.

Authors:  Dey Madhusudan; Agarwal Raju; Nambula Vijaya
Journal:  J Obstet Gynaecol India       Date:  2015-12-17

6.  Remission of congenital complete heart block without anti-Ro/La antibodies: A case report.

Authors:  Souvik Mitra; Anindya Kumar Saha; Syamal Kumar Sardar; Arun Kumarendu Singh
Journal:  Ann Pediatr Cardiol       Date:  2013-07

7.  Spontaneous Remission of Congenital Complete Atrioventricular Block in Anti-Ro/La Antibody-Negative Monozygotic Twins: Case Report.

Authors:  Taner Kasar; Murat Saygı; İsa Özyılmaz; Yakup Ergül
Journal:  Balkan Med J       Date:  2017-01-05       Impact factor: 2.021

8.  First Report of the Italian Registry on Immune-Mediated Congenital Heart Block (Lu.Ne Registry).

Authors:  Micaela Fredi; Laura Andreoli; Beatrice Bacco; Tiziana Bertero; Alessandra Bortoluzzi; Silvia Breda; Veronica Cappa; Fulvia Ceccarelli; Rolando Cimaz; Salvatore De Vita; Emma Di Poi; Elena Elefante; Franco Franceschini; Maria Gerosa; Marcello Govoni; Ariela Hoxha; Andrea Lojacono; Luca Marozio; Alessandro Mathieu; Pier Luigi Meroni; Antonina Minniti; Marta Mosca; Marina Muscarà; Melissa Padovan; Matteo Piga; Roberta Priori; Véronique Ramoni; Amelia Ruffatti; Chiara Tani; Marta Tonello; Laura Trespidi; Sonia Zatti; Stefano Calza; Angela Tincani; Antonio Brucato
Journal:  Front Cardiovasc Med       Date:  2019-02-28

9.  Isolated anti-Ro/La antibody-negative fetal complete atrioventricular block: a case report.

Authors:  Huan-Huan Huo; Ya-Juan Wei; Yan-Hua Qi; Bao-Min Liu
Journal:  Chin Med J (Engl)       Date:  2020-01-05       Impact factor: 2.628

10.  Outcome of Antibody-Mediated Fetal Heart Disease With Standardized Anti-Inflammatory Transplacental Treatment.

Authors:  Wadi Mawad; Lisa Hornberger; Bettina Cuneo; Marie-Josée Raboisson; Anita J Moon-Grady; Jane Lougheed; Karim Diab; Julia Parkman; Earl Silverman; Edgar Jaeggi
Journal:  J Am Heart Assoc       Date:  2022-01-08       Impact factor: 6.106

  10 in total

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