| Literature DB >> 19554811 |
Tulay Guran1, Serap Turan, Behzat Ozkan, Su Gulsun Berrak, Cengiz Canpolat, Tolga Dagli, Funda Sirin Eren, Abdullah Bereket.
Abstract
Ectopic ACTH syndrome (EAS) is extremely rare in the pediatric age group. Sarcomatous tumors causing EAS are even rarer. We report a 9 year-old girl presenting with Cushing's syndrome caused by ectopic ACTH production by a Ewing's sarcoma. This case illustrates that rapid appearance of Cushingoid symptoms, absence of growth retardation and the presence of hypokalemia are suggestive clues for ectopic ACTH production as the source of Cushing's syndrome.Entities:
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Year: 2009 PMID： 19554811 DOI： 10.1515/jpem.2009.22.4.363
Source DB: PubMed Journal: J Pediatr Endocrinol Metab ISSN： 0334-018X Impact factor: 1.634