| Literature DB >> 19373113 |
Suzanne M Yandow1, David L Rimoin, Aimee M Grace, Ramona R Fillman, Ellen M Raney.
Abstract
Treatment of patients with Hutchinson-Gilford progeria syndrome (HGPS) is based on the abnormalities of accelerated aging that affect the healing processes, combined with a fragile cardiovascular status. A classic HGPS case, of Korean ancestry, previously treated for severe coxa valga with bilateral varus osteotomies using blade plate fixation is presented. Complications over the blade plate area required removal of the hardware, after which the patient showed right-sided hypertonicity--determined to be a cerebrovascular accident. Subsequently, the patient returned almost completely to her presurgical neurologic status. Perioperative planning for HGPS patients should include risks that are typically considered in the planning for geriatric patient care.Entities:
Mesh:
Year: 2009 PMID: 19373113 PMCID: PMC2841562 DOI: 10.1097/BPB.0b013e32832ab928
Source DB: PubMed Journal: J Pediatr Orthop B ISSN: 1060-152X Impact factor: 1.041